Progressive retinal degeneration and dysfunction in R6 Huntington's disease mice

Human Molecular Genetics

Volumn 11, Issue 26, 2002, Pages 3351-3359

  Helmlinger, Dominique ^a   Yvert, Gaël ^a,c   Picaud, Serge ^b   Merienne, Karine ^a   Sahel, José ^b   Mandel, Jean Louis ^a   Devys, Didier ^a  

^a INSTITUT DE GÉNÉTIQUE ET DE BIOLOGIE MOLÉCULAIRE ET CELLULAIRE   (France)

^b HÔPITAL SAINT ANTOINE   (France)

^c USA   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

MUTANT PROTEIN; POLYGLUTAMINE;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CELL LOSS; CLINICAL FEATURE; CONTROLLED STUDY; DEGENERATIVE DISEASE; DISEASE SEVERITY; ELECTRORETINOGRAPHY; EYE FUNDUS; GENE EXPRESSION; GENE MUTATION; HUNTINGTON CHOREA; IN VIVO STUDY; MOUSE; MUTANT; NONHUMAN; PHENOTYPE; PHOTORECEPTOR; PRIORITY JOURNAL; RETINA DEGENERATION; RETINA DYSTROPHY; RETINA ROD; RETINOPATHY; SPINOCEREBELLAR DEGENERATION; TRANSGENIC MOUSE; VISUAL DISORDER;

ANIMALS; ANTIBODIES; BLOTTING, WESTERN; DISEASE MODELS, ANIMAL; FLUORESCENT ANTIBODY TECHNIQUE; HUMANS; HUNTINGTON DISEASE; MICE; NERVE TISSUE PROTEINS; NUCLEAR PROTEINS; RETINA; RETINAL DEGENERATION;

ANIMALIA; MUS MUSCULUS;

EID: 0037115495     PISSN: 09646906     EISSN: None     Source Type: Journal    
DOI: 10.1093/hmg/11.26.3351     Document Type: Article

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