Episodic Ataxia Type-1 Mutations in the Kv1.1 Potassium Channel Display Distinct Folding and Intracellular Trafficking Properties

Journal of Biological Chemistry

Volumn 276, Issue 52, 2001, Pages 49427-49434

  Manganas, Louis N ^a   Akhtar, Sobia ^b   Antonucci, Dana E ^a   Campomanes, Claire R ^a   Dolly, J Oliver ^b   Trimmer, James S ^a  

^a STONY BROOK UNIVERSITY   (United States)

^b IMPERIAL COLLEGE LONDON   (United Kingdom)

Author keywords

[No Author keywords available]

Indexed keywords

MUTAGENS; NEUROLOGY; POTASSIUM;

INTRACELLULAR AGGREGATION;

MUTAGENESIS;

ION CHANNEL; POTASSIUM CHANNEL; POTASSIUM ION; TRANSMEMBRANE CONDUCTANCE REGULATOR; VOLTAGE GATED POTASSIUM CHANNEL; KCNA1 CHANNEL; UBIQUITIN; VIMENTIN;

ANIMAL CELL; ARTICLE; ATAXIA; CELL MEMBRANE TRANSPORT; GENE MUTATION; NEUROLOGIC DISEASE; NONHUMAN; PATHOPHYSIOLOGY; POINT MUTATION; POLYACRYLAMIDE GEL ELECTROPHORESIS; POLYMERASE CHAIN REACTION; PRIORITY JOURNAL; PROTEIN FOLDING; ANIMAL; CELL STRAIN COS1; CHEMISTRY; GENETICS; HUMAN; METABOLISM; MUTATION; NERVE CELL; PHENOTYPE; PHYSIOLOGY; POTASSIUM CHANNEL; PROTEIN TRANSPORT; RAT;

ANIMALIA;

ANIMAL; ATAXIA; COS CELLS; HUMAN; MUTATION; NEURONS; PHENOTYPE; POTASSIUM CHANNELS; PROTEIN FOLDING; PROTEIN TRANSPORT; RATS; SUPPORT, NON-U.S. GOV'T; SUPPORT, U.S. GOV'T, P.H.S.; UBIQUITIN; VIMENTIN;

EID: 0035965991     PISSN: 00219258     EISSN: None     Source Type: Journal    
DOI: 10.1074/jbc.M109325200     Document Type: Article

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