Episodic ataxia type-1 mutations in the hKv1.1 cytoplasmic pore region alter the gating properties of the channel

EMBO Journal

Volumn 17, Issue 5, 1998, Pages 1200-1207

  D'Adamo, Maria Cristina ^a   Liu, Zhaoping ^b   Adelman, John P ^c   Maylie, James ^b   Pessia, Mauro ^a  

^a MARIO NEGRI INSTITUTE FOR PHARMACOLOGICAL RESEARCH   (Italy)

^b OREGON HEALTH AND SCIENCE UNIVERSITY   (United States)

^c OREGON HEALTH AND SCIENCE UNIVERSITY   (United States)

Author keywords

Channels; Episodic ataxia type 1; Gating; hKv1.1; Mutation; Potassium channel

Indexed keywords

POTASSIUM CHANNEL; PROTEIN SUBUNIT;

ANIMAL CELL; ARTICLE; ATAXIA; CELL MEMBRANE POTENTIAL; CHANNEL GATING; CODON; CONTROLLED STUDY; EPISODIC ATAXIA TYPE 1; GENE LOCATION; ION CURRENT; NONHUMAN; OOCYTE; POINT MUTATION; PRIORITY JOURNAL; PROTEIN EXPRESSION; XENOPUS;

ANIMALS; ATAXIA; CYTOPLASM; DIMERIZATION; DNA, COMPLEMENTARY; EVOKED POTENTIALS; HUMANS; ION CHANNEL GATING; KINETICS; KV1.1 POTASSIUM CHANNEL; MUTATION; OOCYTES; PATCH-CLAMP TECHNIQUES; POTASSIUM CHANNELS; POTASSIUM CHANNELS, VOLTAGE-GATED; PROTEIN CONFORMATION; RNA, MESSENGER; XENOPUS LAEVIS;

ANIMALIA; ATAXIA;

EID: 0032473349     PISSN: 02614189     EISSN: None     Source Type: Journal    
DOI: 10.1093/emboj/17.5.1200     Document Type: Article

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