Misfolded proteins in the endoplasmic reticulum

Laboratory Investigation

Volumn 79, Issue 6, 1999, Pages 623-638

  Perlmutter, David H ^a  

^a ST LOUIS CHILDREN S HOSPITAL   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

ALPHA 1 ANTITRYPSIN; CELL PROTEIN; CHAPERONE; PROTEASOME; UBIQUITIN;

ALPHA 1 ANTITRYPSIN DEFICIENCY; CHLORIDE TRANSPORT; CYSTIC FIBROSIS; ENDOPLASMIC RETICULUM; GENE TRANSFER; GENOME; HUMAN; PATHOGENESIS; PRIORITY JOURNAL; PROTEIN ASSEMBLY; PROTEIN DEGRADATION; PROTEIN FOLDING; PROTEIN LOCALIZATION; REVIEW; SIGNAL TRANSDUCTION;

ALPHA 1-ANTITRYPSIN DEFICIENCY; ANIMALS; CYSTIC FIBROSIS; CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR; ENDOPLASMIC RETICULUM; GENETIC DISEASES, INBORN; HUMANS; PROTEIN FOLDING; PROTEIN PROCESSING, POST-TRANSLATIONAL;

EID: 0033049537     PISSN: 00236837     EISSN: None     Source Type: Journal    
DOI: None     Document Type: Review

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