Characterization of the structure and the amyloidogenic properties of the Josephin domain of the polyglutamine-containing protein ataxin-3

Journal of Molecular Biology

Volumn 344, Issue 4, 2004, Pages 1021-1035

  Masino, Laura ^a   Nicastro, Giuseppe ^a   Menon, Rajesh P ^a   Piaz, Fabrizio Dal ^b   Calder, Lesley ^a   Pastore, Annalisa ^a  

^a NATIONAL INSTITUTE FOR MEDICAL RESEARCH   (United Kingdom)

^b UNIVERSITY OF BOLOGNA   (Italy)

Author keywords

aggregation; ataxin 3; Josephin; polyglutamine disease; spinocerebellar ataxia type 3

Indexed keywords

ATAXIN 3; POLYGLUTAMINE; PROTEIN DERIVATIVE; UNCLASSIFIED DRUG;

ARTICLE; CARBOXY TERMINAL SEQUENCE; CONTROLLED STUDY; NONHUMAN; PRIORITY JOURNAL; PROTEIN AGGREGATION; PROTEIN ANALYSIS; PROTEIN DETERMINATION; PROTEIN DOMAIN; PROTEIN ISOLATION; PROTEIN MOTIF; PROTEIN STRUCTURE; TEMPERATURE; THERMODYNAMICS;

ATAXIA;

EID: 8544260320     PISSN: 00222836     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.jmb.2004.09.065     Document Type: Article

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