Structural and functional analysis of the Josephin domain of the polyglutamine protein ataxin-3

Biochemical and Biophysical Research Communications

Volumn 322, Issue 2, 2004, Pages 387-394

  Chow, Michelle K M ^a   MacKay, Joel P ^b   Whisstock, James C ^a   Scanlon, Martin J ^c   Bottomley, Stephen P ^a  

^a MONASH UNIVERSITY   (Australia)

^b UNIVERSITY OF SYDNEY   (Australia)

^c MONASH UNIVERSITY   (Australia)

Author keywords

Ataxin 3; Conformational disease; Fibril; Polyglutamine repeat; Protein folding; Protein misfolding

Indexed keywords

ATAXIN 3; POLYGLUTAMINE; PROTEIN; PROTEINASE; UBIQUITIN; UNCLASSIFIED DRUG; ATXN3 PROTEIN, HUMAN; NERVE PROTEIN; NUCLEAR PROTEIN; PEPTIDE; REPRESSOR PROTEIN;

AMINO TERMINAL SEQUENCE; ARTICLE; CONTROLLED STUDY; ENZYME ACTIVITY; NONHUMAN; NUCLEOTIDE SEQUENCE; PRIORITY JOURNAL; PROTEIN ANALYSIS; PROTEIN CONFORMATION; PROTEIN DOMAIN; PROTEIN STRUCTURE; STRUCTURE ANALYSIS; CHEMISTRY; GENETICS; HUMAN; ISOLATION AND PURIFICATION; MACHADO JOSEPH DISEASE; METABOLISM; NUCLEAR MAGNETIC RESONANCE SPECTROSCOPY; PHYSIOLOGY; PROTEIN TERTIARY STRUCTURE; THERMODYNAMICS;

ENDOPEPTIDASES; HUMANS; MACHADO-JOSEPH DISEASE; MAGNETIC RESONANCE SPECTROSCOPY; NERVE TISSUE PROTEINS; NUCLEAR PROTEINS; PEPTIDES; PROTEIN STRUCTURE, TERTIARY; REPRESSOR PROTEINS; THERMODYNAMICS; UBIQUITIN;

EID: 6044269458     PISSN: 0006291X     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.bbrc.2004.07.131     Document Type: Article

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