Structural instability and fibrillar aggregation of non-expanded human ataxin-3 revealed under high pressure and temperature

Journal of Biological Chemistry

Volumn 278, Issue 34, 2003, Pages 31554-31563

  Marchal, Stéphane ^a   Shehi, Erlet ^b   Harricane, Marie Cécile ^c   Fusi, Paola ^b   Heitz, Frédéric ^c   Tortora, Paolo ^b   Lange, Reinhard ^a  

^a INSERM   (France)

^b UNIVERSITY OF MILANO BICOCCA   (Italy)

^c Centre National de la Recherche Scientifique   (France)

Author keywords

[No Author keywords available]

Indexed keywords

ELECTRON MICROSCOPY; FLUORESCENCE; FOURIER TRANSFORM INFRARED SPECTROSCOPY; HIGH PRESSURE EFFECTS; HIGH TEMPERATURE EFFECTS; OLIGOMERS; STRUCTURE (COMPOSITION); ULTRAVIOLET SPECTROSCOPY;

BIOLOGICAL PHENOMENA;

PROTEINS;

8 ANILINO 1 NAPHTHALENESULFONIC ACID; ATAXIN 3; PROTEIN; THIOFLAVINE; UNCLASSIFIED DRUG; WATER;

ARTICLE; BETA SHEET; CIRCULAR DICHROISM; DEGENERATIVE DISEASE; ELECTRON MICROSCOPY; FLUORESCENCE; FOURIER TRANSFORMATION; HIGH TEMPERATURE; HUMAN; HYPERBARISM; NONHUMAN; PRIORITY JOURNAL; PROTEIN AGGREGATION; PROTEIN CONFORMATION; PROTEIN FOLDING; PROTEIN STABILITY; SPECTROSCOPY; TEMPERATURE DEPENDENCE; ULTRAVIOLET SPECTROSCOPY;

AMINO ACID SEQUENCE; ANIMALS; CLONING, MOLECULAR; DNA, COMPLEMENTARY; HEAT; HUMANS; MICE; MOLECULAR SEQUENCE DATA; NERVE TISSUE PROTEINS; NUCLEAR PROTEINS; PRESSURE; PROTEIN CONFORMATION; REPRESSOR PROTEINS; SEQUENCE HOMOLOGY, AMINO ACID; SPECTROMETRY, FLUORESCENCE; SPECTROPHOTOMETRY, ULTRAVIOLET; TRANSCRIPTION FACTORS;

MURINAE;

EID: 0042357191     PISSN: 00219258     EISSN: None     Source Type: Journal    
DOI: 10.1074/jbc.M304205200     Document Type: Article

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