Oxidative stress in urea cycle disorders: Findings from clinical and basic research

Clinica Chimica Acta

Volumn 477, Issue , 2018, Pages 121-126

  Parmeggiani, Belisa ^a   Vargas, Carmen Regla ^a,b  

^a FEDERAL UNIVERSITY OF RIO GRANDE DO SUL   (Brazil)

^b HOSPITAL DE CLÍNICAS DE PORTO ALEGRE   (Brazil)

Author keywords

Inborn errors of metabolism; Nitric oxide; Oxidative stress; Redox balance; Urea cycle disorders

Indexed keywords

AMMONIA; CARGLUMIC ACID; GLUTAMINE; NITRIC OXIDE;

DIET SUPPLEMENTATION; ENZYME DEFICIENCY; HUMAN; IN VITRO STUDY; INBORN ERROR OF METABOLISM; METABOLITE; NITROGEN METABOLISM; NONHUMAN; OXIDATION REDUCTION REACTION; OXIDATIVE STRESS; PRIORITY JOURNAL; PROTEIN BLOOD LEVEL; PROTEIN RESTRICTION; REVIEW; UREA CYCLE; UREA CYCLE DISORDER; ANIMAL; GENETICS; LABORATORY TECHNIQUE; METABOLISM; MUTATION;

ANIMALS; CLINICAL LABORATORY TECHNIQUES; HUMANS; MUTATION; OXIDATIVE STRESS; UREA CYCLE DISORDERS, INBORN;

EID: 85038026784     PISSN: 00098981     EISSN: 18733492     Source Type: Journal    
DOI: 10.1016/j.cca.2017.11.041     Document Type: Review

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