Increased oxidative stress in patients with 3-hydroxy-3-methylglutaric aciduria

Molecular and Cellular Biochemistry

Volumn 402, Issue 1-2, 2015, Pages 149-155

  dos Santos Mello, Mariana ^a,b   Ribas, Graziela Schmitt ^b   Wayhs, Carlos Alberto Yasin ^b   Hammerschmidt, Tatiane ^b   Guerreiro, Gilian Batista Balbueno ^b   Favenzani, Jéssica Lamberty ^b   Sitta, Ângela ^b   de Moura Coelho, Daniella ^b   Wajner, Moacir ^a,b   Vargas, Carmen Regla ^a,b  

^a FEDERAL UNIVERSITY OF RIO GRANDE DO SUL   (Brazil)

^b HOSPITAL DE CLÍNICAS DE PORTO ALEGRE   (Brazil)

Author keywords

3 hydroxy 3 methylglutaric aciduria; Carnitine; Organic acidurias; Oxidative damage; Oxidative stress

Indexed keywords

CARBONYL DERIVATIVE; CARNITINE; CREATININE; PLASMA PROTEIN; THIOBARBITURIC ACID REACTIVE SUBSTANCE; THIOL GROUP; TYROSINE; 3 HYDROXY 3 METHYLGLUTARIC ACID; ACETYL COENZYME A ACETYLTRANSFERASE;

3 HYDROXY 3 METHYLGLUTARIC ACIDURIA; ACIDURIA; ADOLESCENT; ADULT; ARTICLE; BLOOD LEVEL; BLOOD SAMPLING; CLINICAL ARTICLE; CONTROLLED STUDY; CREATININE URINE LEVEL; HUMAN; INFANT; LIPID PEROXIDATION; MIDDLE AGED; OXIDATION; OXIDATIVE STRESS; PROTEIN RESTRICTION; URINALYSIS; URINE LEVEL; YOUNG ADULT; CASE CONTROL STUDY; CHILD; DEFICIENCY; DISORDERS OF AMINO ACID AND PROTEIN METABOLISM; PRESCHOOL CHILD; PROTEIN CARBONYLATION; URINE;

ACETYL-COA C-ACETYLTRANSFERASE; ADOLESCENT; AMINO ACID METABOLISM, INBORN ERRORS; CASE-CONTROL STUDIES; CHILD; CHILD, PRESCHOOL; HUMANS; INFANT; MEGLUTOL; OXIDATIVE STRESS; PROTEIN CARBONYLATION;

EID: 84925485590     PISSN: 03008177     EISSN: 15734919     Source Type: Journal    
DOI: 10.1007/s11010-014-2322-x     Document Type: Article

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