Human Adaptive Immunity Rescues an Inborn Error of Innate Immunity

Cell

Volumn 168, Issue 5, 2017, Pages 789-800.e10

  Israel, Laura ^a,b   Wang, Ying ^c   Bulek, Katarzyna ^d   Della Mina, Erika ^a,b   Zhang, Zhao ^c   Pedergnana, Vincent ^a,b   Chrabieh, Maya ^a,b   Lemmens, Nicole A ^e   Sancho Shimizu, Vanessa ^a,b,f   Descatoire, Marc ^g   Lasseau, Théo ^a,b   Israelsson, Elisabeth ^h   Lorenzo, Lazaro ^a,b   Yun, Ling ^a,b   Belkadi, Aziz ^a,b   Moran, Andrew ⁱ   Weisman, Leonard E ^j   Vandenesch, François ^k   Batteux, Frederic ^l   Weller, Sandra ^g   Levin, Michael ^f   Herberg, Jethro ^f   Abhyankar, Avinash ^m   Prando, Carolina ^m   Itan, Yuval ^m   van Wamel, Willem J B ^e   Picard, Capucine ^a,b,n   Abel, Laurent ^a,b,m   Chaussabel, Damien ^h   Li, Xiaoxia ^d   Beutler, Bruce ^c   Arkwright, Peter D ^o   Casanova, Jean Laurent ^a,b,m,n,p   Puel, Anne ^a,b,m   more..

^a IMAGINE INSTITUTE   (France)

^b UNIVERSITÉ PARIS DESCARTES   (France)

^c UNIVERSITY OF TEXAS SOUTHWESTERN MEDICAL CENTER   (United States)

^d LERNER RESEARCH INSTITUTE   (United States)

^e ERASMUS MEDICAL CENTER   (Netherlands)

^f IMPERIAL COLLEGE LONDON   (United Kingdom)

^g INSTITUT NECKER ENFANTS MALADES   (France)

^h BENAROYA RESEARCH INSTITUTE   (United States)

ⁱ MANCHESTER ROYAL INFIRMARY   (United Kingdom)

^j TEXAS CHILDREN S HOSPITAL   (United States)

^k Hospices Civils de Lyon   (France)

^l Institut Cochin   (France)

^m ROCKEFELLER UNIVERSITY   (United States)

ⁿ HÔPITAL NECKER ENFANTS MALADES   (France)

^o UNIVERSITY OF MANCHESTER   (United Kingdom)

^p HOWARD HUGHES MEDICAL INSTITUTE   (United States)

more..

Author keywords

anti LTA antibodies; incomplete clinical penetrance; lipoteichoic acid; LTA; primary immunodeficiency; staphylococcus aureus; TIRAP; toll like receptors

Indexed keywords

INTERLEUKIN 1 RECEPTOR ASSOCIATED KINASE 4; INTERLEUKIN 6; LIPOTEICHOIC ACID; MESSENGER RNA; MONOCLONAL ANTIBODY; MYELOID DIFFERENTIATION FACTOR 88; TOLL LIKE RECEPTOR 1 AGONIST; TOLL LIKE RECEPTOR 2; TOLL LIKE RECEPTOR 2 AGONIST; TOLL LIKE RECEPTOR 4 AGONIST; TOLL LIKE RECEPTOR 6 AGONIST; TOLL LIKE RECEPTOR AGONIST; TUMOR NECROSIS FACTOR; UNCLASSIFIED DRUG; INTERLEUKIN 1 RECEPTOR; ISOPROTEIN; LIPOPOLYSACCHARIDE; MEMBRANE PROTEIN; MYD88 PROTEIN, HUMAN; TEICHOIC ACID; TIRAP PROTEIN, HUMAN; TLR2 PROTEIN, HUMAN; TOLL LIKE RECEPTOR;

ADAPTIVE IMMUNITY; ALLELE; ANIMAL CELL; ANTIBODY RESPONSE; ARTICLE; AUTOSOMAL RECESSIVE DISORDER; AUTOSOMAL RECESSIVE TIRAP DEFICIENCY; CASE REPORT; CELLULAR DISTRIBUTION; CHILD; CONTROLLED STUDY; DISEASE SEVERITY; FEMALE; FIBROBLAST; GENE MUTATION; HOMOZYGOSITY; HUMAN; HUMAN CELL; IMMUNE DEFICIENCY; IMMUNE RESPONSE; INNATE IMMUNITY; LEUKOCYTE; MACROPHAGE; MOUSE; NONHUMAN; PENETRANCE; PRESCHOOL CHILD; PRIORITY JOURNAL; SCHOOL CHILD; STAPHYLOCOCCUS INFECTION; TIRAP GENE; AGONISTS; DEFICIENCY; GENETICS; IMMUNOLOGY; MALE; METABOLISM; MONOCYTE; PEDIGREE; PHAGOCYTE; POINT MUTATION; STAPHYLOCOCCAL INFECTIONS;

ADAPTIVE IMMUNITY; ANTIBODIES, MONOCLONAL; CHILD; FEMALE; FIBROBLASTS; HUMANS; IMMUNITY, INNATE; LIPOPOLYSACCHARIDES; MACROPHAGES; MALE; MEMBRANE GLYCOPROTEINS; MONOCYTES; MYELOID DIFFERENTIATION FACTOR 88; PEDIGREE; PHAGOCYTES; POINT MUTATION; PROTEIN ISOFORMS; RECEPTORS, INTERLEUKIN-1; STAPHYLOCOCCAL INFECTIONS; TEICHOIC ACIDS; TOLL-LIKE RECEPTOR 2; TOLL-LIKE RECEPTORS;

EID: 85014006510     PISSN: 00928674     EISSN: 10974172     Source Type: Journal    
DOI: 10.1016/j.cell.2017.01.039     Document Type: Article

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