Combined defects in oxidative phosphorylation and fatty acid β-oxidation in Mitochondrial disease

Bioscience Reports

Volumn 36, Issue 2, 2016, Pages

  Nsiah Sefaa, Abena ^a   McKenzie, Matthew ^b  

^a HUDSON INSTITUTE OF MEDICAL RESEARCH   (Australia)

^b MONASH UNIVERSITY   (Australia)

Author keywords

Disease; Mitochondria; Protein complex assembly; Protein interactions; Supercomplex

Indexed keywords

COMPLEX V; CYTOCHROME C OXIDASE; MITOCHONDRIAL ENZYME; REDUCED NICOTINAMIDE ADENINE DINUCLEOTIDE DEHYDROGENASE (UBIQUINONE); SUCCINATE DEHYDROGENASE (UBIQUINONE); UBIQUINOL CYTOCHROME C REDUCTASE; UNCLASSIFIED DRUG; FATTY ACID;

COMPLEX FORMATION; DISORDERS OF MITOCHONDRIAL FUNCTIONS; FAO DISEASE; FATTY ACID OXIDATION; GENE MUTATION; HUMAN; INBORN ERROR OF METABOLISM; MITOCHONDRIAL RESPIRATION; NONHUMAN; OXIDATIVE PHOSPHORYLATION; PATHOGENESIS; PROTEIN ASSEMBLY; PROTEIN INTERACTION; REVIEW; ANIMAL; METABOLISM; MITOCHONDRION; PATHOLOGY;

ANIMALS; FATTY ACIDS; HUMANS; MITOCHONDRIA; MITOCHONDRIAL DISEASES; OXIDATIVE PHOSPHORYLATION;

EID: 84961801095     PISSN: 01448463     EISSN: 15734935     Source Type: Journal    
DOI: 10.1042/BSR20150295     Document Type: Review

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