Impaired amino acid metabolism contributes to fasting-induced hypoglycemia in fatty acid oxidation defects

Human Molecular Genetics

Volumn 22, Issue 25, 2013, Pages 5249-5261

  Houten, Sander M ^a   Herrema, Hilde ^c,f   Brinke, Heleen Te ^a   Denis, Simone ^a   Ruiter, Jos P N ^a   van Dijk, Theo H ^c   Argmann, Carmen A ^b   Ottenhoff, Roelof ^b   Müller, Michael ^e,f   Groen, Albert K ^c,d   Kuipers, Folkert ^c,d   Reijngoud, Dirk Jan ^d   Wanders, Ronald J A ^a  

^a UNIVERSITY OF AMSTERDAM   (Netherlands)

^b ACADEMIC MEDICAL CENTER   (Netherlands)

^c University of Groningen ^*  (United States)

^d UNIVERSITY MEDICAL CENTER GRONINGEN   (Netherlands)

^e WAGENINGEN UNIVERSITY   (Netherlands)

^f TOP INSTITUTE FOOD AND NUTRITION   (Netherlands)

Author keywords

[No Author keywords available]

Indexed keywords

ALANINE; ALANINE AMINOTRANSFERASE; BRANCHED CHAIN AMINO ACID; CARNITINE; FRUCTOSE BISPHOSPHATASE; GLUCOKINASE; GLUCOSE; GLUCOSE 6 PHOSPHATASE; GLUCOSE TRANSPORTER 1; GLUCOSE TRANSPORTER 2; GLUTAMATE AMMONIA LIGASE; GLUTAMINE; GLYCINE; GLYCOGEN PHOSPHORYLASE; GLYCOGEN SYNTHASE; HEART ENZYME; HEXOKINASE; LACTIC ACID; LIVER ENZYME; LONG CHAIN ACYL COENZYME A DEHYDROGENASE; LYSINE; MAMMALIAN TARGET OF RAPAMYCIN; PHOSPHOENOLPYRUVATE CARBOXYKINASE (ATP); PHOSPHOENOLPYRUVATE CARBOXYKINASE (GTP); PROTEIN S6; PYRUVATE CARBOXYLASE; PYRUVATE DEHYDROGENASE KINASE 4; PYRUVATE KINASE; PYRUVIC ACID; SERINE;

ALANINE AMINOTRANSFERASE BLOOD LEVEL; AMINO ACID METABOLISM; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; DIET RESTRICTION; DISORDERS OF AMINO ACID AND PROTEIN METABOLISM; ENZYME ACTIVITY; ENZYME DEFECT; FATTY ACID OXIDATION; GASTROCNEMIUS MUSCLE; GENE EXPRESSION; GLUCONEOGENESIS; GLUCOSE BLOOD LEVEL; GLUCOSE METABOLISM; GLUCOSE SENSOR; GLUCOSE TRANSPORT; GLYCOGEN LIVER LEVEL; HEART; HYPOGLYCEMIA; LIVER; METABOLIC CLEARANCE RATE; MOUSE; NONHUMAN; PRIORITY JOURNAL; PROTEIN DEGRADATION; PROTEIN HOMEOSTASIS; PROTEIN PHOSPHORYLATION; REAL TIME POLYMERASE CHAIN REACTION; SOLEUS MUSCLE;

ACYL-COA DEHYDROGENASE, LONG-CHAIN; AMINO ACIDS; ANIMALS; DISEASE MODELS, ANIMAL; FATTY ACIDS; GLUCONEOGENESIS; GLUCOSE; HUMANS; HYPOGLYCEMIA; LIPID METABOLISM, INBORN ERRORS; LIVER GLYCOGEN; MICE; MICE, KNOCKOUT; MITOCHONDRIA, LIVER; OXIDATION-REDUCTION;

EID: 84887896439     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/ddt382     Document Type: Article

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