Human Trifunctional Protein Alpha Links Cardiolipin Remodeling to Beta-Oxidation

PLoS ONE

Volumn 7, Issue 11, 2012, Pages

  Taylor, William A ^a   Mejia, Edgard M ^a   Mitchell, Ryan W ^a   Choy, Patrick C ^a   Sparagna, Genevieve C ^b   Hatch, Grant M ^a  

^a UNIVERSITY OF MANITOBA   (Canada)

^b UNIVERSITY OF COLORADO   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

ACYL COENZYME A; ALPHA SUBUNIT OF TRIFUNCTIONAL PROTEIN; CARDIOLIPIN; COENZYME A; LINOLEIC ACID; LINOLEOYL COENZYME A DESATURASE; LYSOPHOSPHOLIPID; MESSENGER RNA; MONOLYSOCARDIOLIPIN; OLEIC ACID; PALMITIC ACID; PHOSPHOLIPID; RECOMBINANT PROTEIN; UNCLASSIFIED DRUG;

ACYLATION; ALPHA SUBUNIT OF TRIFUNCTIONAL GENE; AMINO ACID SEQUENCE; ARTICLE; BARTH SYNDROME; CONTROLLED STUDY; DOWN REGULATION; ENZYME ACTIVITY; ENZYME ASSAY; FATTY ACID OXIDATION; GENE; GENE EXPRESSION REGULATION; GENE IDENTIFICATION; GENE SILENCING; HELA CELL; HUMAN; IN VITRO STUDY; MITOCHONDRIAL RESPIRATION; MITOCHONDRIAL TARGETING SIGNAL; MONOLYSOCARDIOPILIN ACYLTRANSFERASE 1 GENE; NONHUMAN; NUCLEOTIDE SEQUENCE; PROTEIN DETERMINATION; PROTEIN EXPRESSION; PROTEIN FUNCTION; PROTEIN METABOLISM; PROTEIN SYNTHESIS; RAT; RESPIRATORY CHAIN; RNA INTERFERENCE; SEQUENCE ALIGNMENT; UPREGULATION; WESTERN BLOTTING;

ACYL COENZYME A; ACYLTRANSFERASES; AMINO ACID SEQUENCE; ANIMALS; CARDIOLIPINS; CELL LINE; ENZYME ACTIVATION; FATTY ACIDS; GENE EXPRESSION; GENE EXPRESSION REGULATION; HUMANS; LYSOPHOSPHOLIPIDS; MALE; MOLECULAR SEQUENCE DATA; MULTIENZYME COMPLEXES; OXIDATION-REDUCTION; PALMITOYL COENZYME A; PROTEIN BINDING; RATS; RECOMBINANT FUSION PROTEINS; RNA INTERFERENCE; SEQUENCE ALIGNMENT; SUBSTRATE SPECIFICITY; THYROXINE;

EID: 84869054528     PISSN: None     EISSN: 19326203     Source Type: Journal    
DOI: 10.1371/journal.pone.0048628     Document Type: Article

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