Polymers of Z α1-antitrypsin are secreted in cell models of disease

European Respiratory Journal

Volumn 47, Issue 3, 2016, Pages 1005-1009

  Fra, Annamaria ^a   Cosmi, Francesca ^b   Ordoñez, Adriana ^c   Berardelli, Romina ^a   Perez, Juan ^d   Guadagno, Noemi A ^b   Corda, Luciano ^e   Marciniak, Stefan J ^c   Lomas, David A ^f   Miranda, Elena ^b,g  

^a UNIVERSITY OF BRESCIA   (Italy)

^b SAPIENZA UNIVERSITY OF ROME   (Italy)

^c UNIVERSITY OF CAMBRIDGE   (United Kingdom)

^d UNIVERSITY OF MÁLAGA   (Spain)

^e SPEDALI CIVILI   (Italy)

^f UNIVERSITY COLLEGE LONDON   (United Kingdom)

^g SAPIENZA UNIVERSITY OF ROME   (Italy)

Author keywords

[No Author keywords available]

Indexed keywords

ALPHA 1 ANTITRYPSIN; EPITOPE; HEMAGGLUTININ; MUTANT PROTEIN; MYC PROTEIN; POLYMER; IMMUNOLOGIC FACTOR;

ANIMAL CELL; ANTIBODY SPECIFICITY; CELL CULTURE; CELLULAR DISEASE MODEL; CHO CELL LINE; COMPLEX FORMATION; CULTURE MEDIUM; DISEASE MODEL; ENDOPLASMIC RETICULUM; GOLGI COMPLEX; HEK293 CELL LINE; HUMAN; HUMAN CELL; IMMUNOFLUORESCENCE; LETTER; LIVER CELL; NONHUMAN; POLYACRYLAMIDE GEL ELECTROPHORESIS; PRIORITY JOURNAL; PROTEIN DEFICIENCY; PROTEIN EXPRESSION; PROTEIN GLYCOSYLATION; PROTEIN LOCALIZATION; PROTEIN POLYMERIZATION; PROTEIN SECRETION; PROTEIN SYNTHESIS; PROTEIN TRANSPORT; ALLELE; ALPHA 1 ANTITRYPSIN DEFICIENCY; BLOOD; MUTATION; PROTEIN MULTIMERIZATION; TRANSPORT AT THE CELLULAR LEVEL;

ALLELES; ALPHA 1-ANTITRYPSIN; ALPHA 1-ANTITRYPSIN DEFICIENCY; BIOLOGICAL TRANSPORT; HEK293 CELLS; HUMANS; IMMUNOLOGIC FACTORS; MUTATION; PROTEIN MULTIMERIZATION;

EID: 84959908718     PISSN: 09031936     EISSN: 13993003     Source Type: Journal    
DOI: 10.1183/13993003.00940-2015     Document Type: Letter

References (13)

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