Characterising the neuropathology and neurobehavioural phenotype in friedreich ataxia a systematic review

Advances in Experimental Medicine and Biology

Volumn 769, Issue , 2012, Pages 169-184

  Corben, Louise A ^a   Georgiou Karistianis, Nellie ^b   Bradshaw, John L ^b   Evans Galea, Marguerite V ^a   Churchyard, Andrew J ^c   Delatycki, Martin B ^a,d,e  

^a ROYAL CHILDREN'S HOSPITAL   (Australia)

^b MONASH UNIVERSITY   (Australia)

^c MONASH MEDICAL CENTRE   (Australia)

^d AUSTIN HEALTH   (Australia)

^e UNIVERSITY OF MELBOURNE   (Australia)

Author keywords

[No Author keywords available]

Indexed keywords

FRATAXIN; HISTONE DEACETYLASE INHIBITOR;

BRAIN ATROPHY; CEREBELLAR ATAXIA; COGNITIVE DEFECT; DENTATE NUCLEUS; DISEASE SEVERITY; DYSARTHRIA; EPIGENETICS; EXECUTIVE FUNCTION; FRIEDREICH ATAXIA; FRIEDREICH ATAXIA WITH RETAINED REFLEXES; FXN GENE; GENOTYPE PHENOTYPE CORRELATION; HOMOZYGOSITY; HUMAN; INTELLIGENCE; LATE ONSET FRIEDREICH ATAXIA; MOLECULAR GENETICS; MOTOR CONTROL; NEUROBIOLOGY; NEUROIMAGING; NEUROPATHOLOGY; NUCLEAR MAGNETIC RESONANCE IMAGING; PRIORITY JOURNAL; REVIEW; SYSTEMATIC REVIEW; TRINUCLEOTIDE REPEAT; BEHAVIOR; CARDIOMYOPATHY; CLINICAL FEATURE; COGNITION; GENETIC VARIABILITY; IRON HOMEOSTASIS; MOTOR PERFORMANCE; NONHUMAN; PHENOTYPE; SCOLIOSIS; TRACTOGRAPHY; TRANSCRANIAL MAGNETIC STIMULATION;

EID: 84934442223     PISSN: 00652598     EISSN: None     Source Type: Book Series    
DOI: 10.1007/978-1-4614-5434-2_11     Document Type: Review

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