ERdj3 is an endoplasmic reticulum degradation factor for mutant glucocerebrosidase variants linked to Gaucher's disease

Chemistry and Biology

Volumn 21, Issue 8, 2014, Pages 967-976

  Tan, Yun Lei ^a   Genereux, Joseph C ^a   Pankow, Sandra ^a   Aerts, Johannes M F G ^b   Yates, John R ^a   Kelly, Jeffery W ^a  

^a SCRIPPS RESEARCH INSTITUTE   (United States)

^b ACADEMIC MEDICAL CENTER   (Netherlands)

Author keywords

[No Author keywords available]

Indexed keywords

CALCIUM; CALNEXIN; DILTIAZEM; GLUCOSYLCERAMIDASE; HEAT SHOCK PROTEIN; PROTEIN ERDJ3; UNCLASSIFIED DRUG; DNAJB11 PROTEIN, HUMAN; HEAT SHOCK PROTEIN 40; MUTANT PROTEIN;

ARTICLE; CONTROLLED STUDY; ENDOPLASMIC RETICULUM; ENZYME DEGRADATION; FIBROBLAST; GAUCHER DISEASE; HELA CELL LINE; HUMAN; HUMAN CELL; IMMUNOPRECIPITATION; LYSOSOME; MASS SPECTROMETRY; PRIORITY JOURNAL; PROTEIN DEPLETION; PROTEIN FOLDING; PROTEIN FUNCTION; PROTEIN HOMEOSTASIS; PROTEIN INTERACTION; PROTEOMICS; QUALITY CONTROL; CELL CULTURE; DEFICIENCY; ENZYMOLOGY; GENETICS; METABOLISM; MUTATION;

CELLS, CULTURED; ENDOPLASMIC RETICULUM; GAUCHER DISEASE; GLUCOSYLCERAMIDASE; HELA CELLS; HSP40 HEAT-SHOCK PROTEINS; HUMANS; IMMUNOPRECIPITATION; MASS SPECTROMETRY; MUTANT PROTEINS; MUTATION; PROTEIN FOLDING; PROTEOMICS;

EID: 84920439211     PISSN: 10745521     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.chembiol.2014.06.008     Document Type: Article

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