Ca2+ homeostasis modulation enhances the amenability of L444P glucosylcerebrosidase to proteostasis regulation in patient-derived fibroblasts

ACS Chemical Biology

Volumn 6, Issue 2, 2011, Pages 158-168

  Wang, Fan ^a   Agnello, Giulia ^a   Sotolongo, Natasha ^b   Segatori, Laura ^a,b  

^a Rice University   (United States)

^b RICE UNIVERSITY   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

1,1' DIHEPTYL 4,4' BIPYRIDINIUM DIBROMIDE; BENZYLOXYCARBONYLLEUCYLLEUCYLLEUCINAL; CALCIUM CHANNEL BLOCKING AGENT; CALCIUM ION; DANTROLENE; GLUCOSE REGULATED PROTEIN 78; GLUCOSYLCERAMIDASE; RUTHENIUM RED; RYANODINE; THAPSIGARGIN; UNCLASSIFIED DRUG; CALCIUM; DIVALENT CATION; PROTEIN; RYANODINE RECEPTOR;

ARTICLE; BIOGENESIS; CALCIUM HOMEOSTASIS; CELL MIGRATION; CONTROLLED STUDY; CYTOTOXICITY; ENDOPLASMIC RETICULUM; FIBROBLAST; GAUCHER DISEASE; GENE EXPRESSION PROFILING; HUMAN; HUMAN CELL; PRIORITY JOURNAL; PROTEIN FOLDING; PROTEIN HOMEOSTASIS; CELL LINE; CHEMISTRY; ENZYMOLOGY; GENETIC VARIABILITY; GENETICS; HOMEOSTASIS; LYSOSOME; METABOLISM; NERVE CELL;

CALCIUM; CATIONS, DIVALENT; CELL LINE; ENDOPLASMIC RETICULUM; FIBROBLASTS; GAUCHER DISEASE; GENE EXPRESSION PROFILING; GENETIC VARIATION; GLUCOSYLCERAMIDASE; HOMEOSTASIS; HUMANS; LYSOSOMES; NEURONS; PROTEINS; RYANODINE RECEPTOR CALCIUM RELEASE CHANNEL;

EID: 79951933202     PISSN: 15548929     EISSN: 15548937     Source Type: Journal    
DOI: 10.1021/cb100321m     Document Type: Article

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