Haemolysis and perturbations in the systemic iron metabolism of suckling, copper-deficient mosaic mutant mice - An animal model of menkes disease

PLoS ONE

Volumn 9, Issue 9, 2014, Pages

  Lenartowicz, Małgorzata ^a   Starzyński, Rafał R ^b   Krzeptowski, Wojciech ^a   Grzmil, Paweł ^a   Bednarz, Aleksandra ^a   Ogórek, Mateusz ^a   Pierzchała, Olga ^a   Staroń, Robert ^b   Gajowiak, Anna ^b   Lipiński, Paweł ^b  

^a JAGIELLONIAN UNIVERSITY   (Poland)

^b INSTITUTE OF GENETICS AND ANIMAL BREEDING   (Poland)

Author keywords

[No Author keywords available]

Indexed keywords

COPPER ZINC SUPEROXIDE DISMUTASE; FERROPORTIN; HAPTOGLOBIN; HEME OXYGENASE 1; HEMOGLOBIN; HEPCIDIN; ADENOSINE TRIPHOSPHATASE; ATP7A PROTEIN, MOUSE; CATION TRANSPORT PROTEIN; COPPER; HMOX1 PROTEIN, MOUSE; IRON; MEMBRANE PROTEIN; METAL TRANSPORTING PROTEIN 1; SUPEROXIDE DISMUTASE;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; COPPER DEFICIENCY; ENZYME ACTIVITY; ENZYME INDUCTION; ENZYME LOCALIZATION; ERYTHROCYTE; FEMALE; GENE EXPRESSION; HEMOLYSIS; IRON METABOLISM; KIDNEY; LIVER; MALE; MENKES SYNDROME; MOUSE; MOUSE MUTANT; NONHUMAN; PROTEIN BLOOD LEVEL; PROTEIN DEPLETION; PROTEIN EXPRESSION; ANIMAL; BLOOD; CELL LINE; DISEASE MODEL; GENE EXPRESSION REGULATION; GENETICS; HUMAN; METABOLISM; MUTATION; PATHOLOGY;

ANIMALIA; MUS;

ADENOSINE TRIPHOSPHATASES; ANIMALS; CATION TRANSPORT PROTEINS; CELL LINE; COPPER; DISEASE MODELS, ANIMAL; ERYTHROCYTES; FEMALE; GENE EXPRESSION REGULATION; HEME OXYGENASE-1; HEMOLYSIS; HEPCIDINS; HUMANS; IRON; KIDNEY; LIVER; MALE; MEMBRANE PROTEINS; MENKES KINKY HAIR SYNDROME; MICE; MUTATION; SUPEROXIDE DISMUTASE;

EID: 84907573474     PISSN: None     EISSN: 19326203     Source Type: Journal    
DOI: 10.1371/journal.pone.0107641     Document Type: Article

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