Partial complex I deficiency due to the CNS conditional ablation of Ndufa5 results in a mild chronic encephalopathy but no increase in oxidative damage

Human Molecular Genetics

Volumn 23, Issue 6, 2014, Pages 1399-1412

  Peralta, Susana ^a   Torraco, Alessandra ^a,b   Wenz, Tina ^a,c,d   Garcia, Sofia ^a   Diaz, Francisca ^a   Moraes, Carlos T ^a  

^a UNIVERSITY OF MIAMI MILLER SCHOOL OF MEDICINE   (United States)

^b BAMBINO GESÙ CHILDREN S HOSPITAL   (Italy)

^c UNIVERSITY OF COLOGNE   (Germany)

^d German Network for Mitochondrial Disorders (mitoNET)   (Germany)

Author keywords

[No Author keywords available]

Indexed keywords

ANIMALS; BRAIN DAMAGE, CHRONIC; CEREBRAL CORTEX; DISEASE MODELS, ANIMAL; DNA DAMAGE; ELECTRON TRANSPORT COMPLEX I; EMBRYO, MAMMALIAN; MICE; MICE, KNOCKOUT; NADH DEHYDROGENASE; NEURONS; OXIDATIVE STRESS;

EID: 84894363141     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/ddt526     Document Type: Article

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