Overexpression of survival motor neuron improves neuromuscular function and motor neuron survival in mutant SOD1 mice

Neurobiology of Aging

Volumn 35, Issue 4, 2014, Pages 906-915

  Turner, Bradley J ^a   Alfazema, Neza ^b   Sheean, Rebecca K ^a   Sleigh, James N ^b,c   Davies, Kay E ^b   Horne, Malcolm K ^a   Talbot, Kevin ^b,c  

^a UNIVERSITY OF MELBOURNE   (Australia)

^b UNIVERSITY OF OXFORD   (United Kingdom)

^c UNIVERSITY OF OXFORD   (United Kingdom)

Author keywords

Amyotrophic lateral sclerosis; Spinal muscular atrophy; Superoxide dismutase 1; Survival motor neuron

Indexed keywords

SURVIVAL MOTOR NEURON PROTEIN;

ADULT; AGED; AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL BEHAVIOR; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; ASTROCYTOSIS; CELL COUNT; CELL SURVIVAL; CLINICAL ARTICLE; CONTROLLED STUDY; FEMALE; GENE OVEREXPRESSION; HUMAN; LOCOMOTION; MALE; MIDDLE AGED; MOTONEURON; MOUSE; NEUROMUSCULAR FUNCTION; NONHUMAN; PRIORITY JOURNAL; PROTEIN BLOOD LEVEL; PROTEIN DEPLETION; PROTEIN FUNCTION; PROTEIN LOCALIZATION; SPINAL CORD; UPREGULATION; VERY ELDERLY;

AMYOTROPHIC LATERAL SCLEROSIS; SPINAL MUSCULAR ATROPHY; SUPEROXIDE DISMUTASE 1; SURVIVAL MOTOR NEURON;

ADULT; AGED; AGED, 80 AND OVER; AMYOTROPHIC LATERAL SCLEROSIS; ANIMALS; CELL SURVIVAL; DISEASE MODELS, ANIMAL; FEMALE; GENE EXPRESSION; HUMANS; MALE; MICE, TRANSGENIC; MIDDLE AGED; MOTOR ACTIVITY; MOTOR NEURONS; MUSCULAR ATROPHY, SPINAL; MUTATION; SPINAL CORD; SUPEROXIDE DISMUTASE; SURVIVAL OF MOTOR NEURON 1 PROTEIN; UP-REGULATION;

EID: 84891373339     PISSN: 01974580     EISSN: 15581497     Source Type: Journal    
DOI: 10.1016/j.neurobiolaging.2013.09.030     Document Type: Article

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