Survival motor neuron deficiency enhances progression in an amyotrophic lateral sclerosis mouse model

Neurobiology of Disease

Volumn 34, Issue 3, 2009, Pages 511-517

  Turner, Bradley J ^a,b   Parkinson, Nicholas J ^a   Davies, Kay E ^a   Talbot, Kevin ^a  

^a UNIVERSITY OF OXFORD   (United Kingdom)

^b UNIVERSITY OF MELBOURNE   (Australia)

Author keywords

Amyotrophic lateral sclerosis; Motor neuron; Ribonuclear protein; Spinal muscular atrophy; Superoxide dismutase 1; Survival motor neuron

Indexed keywords

PARAQUAT; SURVIVAL MOTOR NEURON PROTEIN;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; DISEASE COURSE; FAMILIAL DISEASE; GENE; GENE DISRUPTION; GENE EXPRESSION REGULATION; GENE MUTATION; GENETIC ASSOCIATION; GENOTYPE; MOTOR PERFORMANCE; MOUSE; NERVE CELL CULTURE; NONHUMAN; PHENOTYPE; PRIORITY JOURNAL; PROTEIN DEFICIENCY; SMN GENE; SMN1 GENE; SMN2 GENE; SOD1 GENE; SPINAL CORD; SPINAL MUSCULAR ATROPHY;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMALS; CELL LINE; CELL NUCLEUS; DISEASE MODELS, ANIMAL; DISEASE PROGRESSION; FEMALE; MALE; MICE; MICE, KNOCKOUT; MICE, TRANSGENIC; MUTATION, MISSENSE; NEURONS; OXIDANTS; PARAQUAT; RNA, MESSENGER; SPINAL CORD; SUPEROXIDE DISMUTASE; SURVIVAL OF MOTOR NEURON 1 PROTEIN;

EID: 67349285905     PISSN: 09699961     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.nbd.2009.03.005     Document Type: Article

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