Nuclear localization of human SOD1 and mutant SOD1-specific disruption of survival motor neuron protein complex in transgenic amyotrophic lateral sclerosis mice

Journal of Neuropathology and Experimental Neurology

Volumn 71, Issue 2, 2012, Pages 162-177

  Gertz, Barry ^a,b   Wong, Margaret ^a   Martin, Lee J ^a,b,c  

^a Department of Pathology ^*  (United States)

^b Pathobiology Graduate Program   (United States)

^c JOHNS HOPKINS UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

Cajal body; Gemin 1; Nuclear gems; Snurportin; Spinal muscular atrophy

Indexed keywords

COPPER ZINC SUPEROXIDE DISMUTASE; MUTANT PROTEIN;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CELL NUCLEUS; COILED BODY; CONTROLLED STUDY; FAMILIAL DISEASE; GENE MUTATION; MOTONEURON; MOTOR NEURON DISEASE; MOUSE; NEUROPATHOLOGY; NONHUMAN; PRIORITY JOURNAL; PROTEIN LOCALIZATION; SPINAL MUSCULAR ATROPHY; SURVIVAL; TRANSGENIC MOUSE;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMALS; CELL NUCLEUS; CENTRAL NERVOUS SYSTEM; DISEASE MODELS, ANIMAL; HUMANS; MICE; MICE, TRANSGENIC; MOTOR NEURONS; MUTATION; SUPEROXIDE DISMUTASE;

EID: 84856051539     PISSN: 00223069     EISSN: 15546578     Source Type: Journal    
DOI: 10.1097/NEN.0b013e318244b635     Document Type: Article

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