Breathing challenges in Rett Syndrome: Lessons learned from humans and animal models

Respiratory Physiology and Neurobiology

Volumn 189, Issue 2, 2013, Pages 280-287

  Ramirez, Jan Marino ^a,b   Ward, Christopher Scott ^c,d   Neul, Jeffrey Lorenz ^c,d  

^a SEATTLE CHILDREN S RESEARCH INSTITUTE   (United States)

^b UNIVERSITY OF WASHINGTON SCHOOL OF MEDICINE   (United States)

^c BAYLOR COLLEGE OF MEDICINE   (United States)

^d TEXAS CHILDREN S HOSPITAL   (United States)

Author keywords

Dysautonomia; Mecp2; Pre Boetzinger Complex

Indexed keywords

4 AMINOBUTYRIC ACID; BRAIN DERIVED NEUROTROPHIC FACTOR; DESIPRAMINE; DOPAMINE; METHYL CPG BINDING PROTEIN 2; NEUROTRANSMITTER RECEPTOR; NORADRENALIN; SEROTONIN; SEROTONIN 1A RECEPTOR;

APNEA; BREATH HOLDING; BREATHING; BREATHING DISORDER; BREATHING PATTERN; BREATHING RATE; DISEASE COURSE; DISEASE DURATION; DISEASE SEVERITY; DYSAUTONOMIA; GENE EXPRESSION; GENETIC ASSOCIATION; GLIA CELL; HEART RATE; HUMAN; HYPERVENTILATION; HYPOVENTILATION; HYPOXEMIA; NERVE CELL NETWORK; NEUROMODULATION; NONHUMAN; NUCLEAR LOCALIZATION SIGNAL; NULL ALLELE; PONS; PRIORITY JOURNAL; RESPIRATION CENTER; RETT SYNDROME; REVIEW; SLEEP; SLEEP DISORDERED BREATHING; SYNAPTIC TRANSMISSION; VALSALVA MANEUVER; WAKEFULNESS;

DYSAUTONOMIA; MECP2; PRE-BOETZINGER COMPLEX;

ANIMALS; DISEASE MODELS, ANIMAL; HUMANS; MICE; NERVE NET; RESPIRATION DISORDERS; RESPIRATORY MECHANICS; RETT SYNDROME;

EID: 84886239167     PISSN: 15699048     EISSN: 18781519     Source Type: Journal    
DOI: 10.1016/j.resp.2013.06.022     Document Type: Review

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