The negative impact of α-ketoglutarate dehydrogenase complex deficiency on matrix substrate-level phosphorylation

FASEB Journal

Volumn 27, Issue 6, 2013, Pages 2393-2406

  Kiss, Gergely ^a   Konrad, Csaba ^a   Doczi, Judit ^a   Starkov, Anatoly A ^b   Kawamata, Hibiki ^b   Manfredi, Giovanni ^b   Zhang, Steven F ^b   Gibson, Gary E ^c   Beal, M Flint ^b   Adam Vizi, Vera ^a   Chinopoulos, Christos ^a,b  

^a SEMMELWEIS UNIVERSITY   (Hungary)

^b WEILL CORNELL MEDICAL COLLEGE   (United States)

^c BURKE MEDICAL RESEARCH INSTITUTE   (United States)

Author keywords

Adenine nucleotide translocase; F0 F 1 ATP synthase; Reversal potential; Succinyl CoA ligase

Indexed keywords

ADENINE NUCLEOTIDE TRANSLOCASE; ADENOSINE TRIPHOSPHATE; DIHYDROLIPOAMIDE DEHYDROGENASE; OXOGLUTARATE DEHYDROGENASE; SUCCINYL COENZYME A SYNTHETASE; ACYLTRANSFERASE; DIHYDROLIPOAMIDE SUCCINYLTRANSFERASE;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; ENZYME ACTIVITY; EXTRACELLULAR MATRIX; FEMALE; IMMUNOREACTIVITY; IN SITU HYBRIDIZATION; MALE; MITOCHONDRIAL RESPIRATION; MITOCHONDRION; NONHUMAN; PRIORITY JOURNAL; PROTEIN PHOSPHORYLATION; TRANSGENIC MOUSE; WESTERN BLOTTING; 129 MOUSE; ANIMAL; C57BL MOUSE; CHEMISTRY; DISORDERS OF AMINO ACID AND PROTEIN METABOLISM; ENZYME SPECIFICITY; F0-F1 ATP SYNTHASE; GENETICS; METABOLISM; MOUSE; PHOSPHORYLATION; REVERSAL POTENTIAL; SUCCINYL-COA LIGASE;

MUS; MUS MUSCULUS;

ADENINE NUCLEOTIDE TRANSLOCASE; F0-F1 ATP SYNTHASE; REVERSAL POTENTIAL; SUCCINYL-COA LIGASE;

ACYLTRANSFERASES; AMINO ACID METABOLISM, INBORN ERRORS; ANIMALS; DIHYDROLIPOAMIDE DEHYDROGENASE; FEMALE; KETOGLUTARATE DEHYDROGENASE COMPLEX; MALE; MICE; MICE, 129 STRAIN; MICE, INBRED C57BL; MICE, TRANSGENIC; PHOSPHORYLATION; SUBSTRATE SPECIFICITY;

MLCS; MLOWN;

EID: 84878753008     PISSN: None     EISSN: 15306860     Source Type: Journal    
DOI: 10.1096/fj.12-220202     Document Type: Article

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