Wolfram Syndrome protein, Miner1, regulates sulphydryl redox status, the unfolded protein response, and Ca2+ homeostasis

EMBO Molecular Medicine

Volumn 5, Issue 6, 2013, Pages 904-918

  Wiley, Sandra E ^a   Andreyev, Alexander Y ^a   Divakaruni, Ajit S ^a   Karisch, Robert ^b   Perkins, Guy ^a   Wall, Estelle A ^a   van der Geer, Peter ^c   Chen, Yi Fan ^d   Tsai, Ting Fen ^d   Simon, Melvin I ^a   Neel, Benjamin G ^b   Dixon, Jack E ^a,e,f   Murphy, Anne N ^a  

^a UNIVERSITY OF CALIFORNIA   (United States)

^b UNIVERSITY HEALTH NETWORK   (Canada)

^c SAN DIEGO STATE UNIVERSITY   (United States)

^d NATIONAL YANG MING UNIVERSITY   (Taiwan)

^e UNIVERSITY OF CALIFORNIA   (United States)

^f HOWARD HUGHES MEDICAL INSTITUTE   (United States)

Author keywords

Calcium; Endoplasmic reticulum; Mitochondria; Oxidative stress; Wolfram Syndrome

Indexed keywords

ACETYLCYSTEINE; ADENOSINE DIPHOSPHATE; ADENOSINE TRIPHOSPHATE; CALCIUM ION; CALNEXIN; GLUCOSE REGULATED PROTEIN 78; GLUTATHIONE; GLUTATHIONE DISULFIDE; GROWTH ARREST AND DNA DAMAGE INDUCIBLE PROTEIN 153; HISTAMINE; MEMBRANE PROTEIN; MESSENGER RNA; MINER1 PROTEIN; NICOTINAMIDE ADENINE DINUCLEOTIDE; PROTEIN IRE1; REACTIVE NITROGEN SPECIES; REACTIVE OXYGEN METABOLITE; REDUCED NICOTINAMIDE ADENINE DINUCLEOTIDE; TRYPSIN; UNCLASSIFIED DRUG;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CALCIUM DEPLETION; CALCIUM HOMEOSTASIS; CELL STRUCTURE; CELL ULTRASTRUCTURE; CONTROLLED STUDY; EMBRYO; ENDOPLASMIC RETICULUM; ENDOPLASMIC RETICULUM STRESS; FIBROBLAST; GENE DELETION; GENE EXPRESSION; MITOCHONDRIAL MEMBRANE; MITOCHONDRIAL RESPIRATION; MITOCHONDRION; MOUSE; NONHUMAN; OXIDATION REDUCTION STATE; OXIDATIVE STRESS; PHENOTYPE; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN LOCALIZATION; RAT; UNFOLDED PROTEIN RESPONSE; WOLFRAM SYNDROME;

ADENOSINE TRIPHOSPHATE; ANIMALS; ANTIOXIDANTS; CALCIUM; CARRIER PROTEINS; CELL LINE; GLUTATHIONE; GLUTATHIONE DISULFIDE; MICE; MITOCHONDRIA; NAD; NERVE TISSUE PROTEINS; OXIDATION-REDUCTION; SULFHYDRYL COMPOUNDS; UNFOLDED PROTEIN RESPONSE; WOLFRAM SYNDROME;

EID: 84878678015     PISSN: 17574676     EISSN: 17574684     Source Type: Journal    
DOI: 10.1002/emmm.201201429     Document Type: Article

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