-
2
-
-
0028092958
-
Nitric oxide synthases: Roles, tolls, and controls
-
Nathan, C.; Xie, Q.W. Nitric oxide synthases: Roles, tolls, and controls. Cell 1994, 78, 915-918.
-
(1994)
Cell
, vol.78
, pp. 915-918
-
-
Nathan, C.1
Xie, Q.W.2
-
3
-
-
77956012154
-
Nitric oxide and neuronal death
-
Brown, G.C. Nitric oxide and neuronal death. Nitric Oxide 2010, 23, 153-165.
-
(2010)
Nitric Oxide
, vol.23
, pp. 153-165
-
-
Brown, G.C.1
-
4
-
-
4944260285
-
Mitochondrial disorders
-
Zeviani, M.; di Donato, S. Mitochondrial disorders. Brain 2004, 127, 2153-2172.
-
(2004)
Brain
, vol.127
, pp. 2153-2172
-
-
Zeviani, M.1
di Donato, S.2
-
5
-
-
84858376953
-
Mitochondria: In sickness and in health
-
Nunnari, J.; Suomalainen, A. Mitochondria: In sickness and in health. Cell 2012, 148, 1145-1159.
-
(2012)
Cell
, vol.148
, pp. 1145-1159
-
-
Nunnari, J.1
Suomalainen, A.2
-
6
-
-
77955330843
-
A neurological perspective on mitochondrial disease
-
McFarland, R.; Taylor, R.W.; Turnbull, D.M. A neurological perspective on mitochondrial disease. Lancet Neurol. 2010, 9, 829-840.
-
(2010)
Lancet Neurol.
, vol.9
, pp. 829-840
-
-
McFarland, R.1
Taylor, R.W.2
Turnbull, D.M.3
-
7
-
-
0025666322
-
A mutation in the tRNA(Leu)(UUR) gene associated with the MELAS subgroup of mitochondrial encephalomyopathies
-
Goto, Y.; Nonaka, I.; Horai, S. A mutation in the tRNA(Leu)(UUR) gene associated with the MELAS subgroup of mitochondrial encephalomyopathies. Nature 1990, 348, 651-653.
-
(1990)
Nature
, vol.348
, pp. 651-653
-
-
Goto, Y.1
Nonaka, I.2
Horai, S.3
-
8
-
-
54949142139
-
Mitochondrial encephalopathy, lactic acidosis, and strokelike episodes: Basic concepts, clinical phenotype, and therapeutic management of melas syndrome
-
Sproule, D.M.; Kaufmann, P. Mitochondrial encephalopathy, lactic acidosis, and strokelike episodes: Basic concepts, clinical phenotype, and therapeutic management of melas syndrome. Ann. N. Y. Acad. Sci. 2008, 1142, 133-158.
-
(2008)
Ann. N.Y. Acad. Sci.
, vol.1142
, pp. 133-158
-
-
Sproule, D.M.1
Kaufmann, P.2
-
9
-
-
33745648369
-
Endothelial dysfunction in melas improved by L-arginine supplementation
-
Koga, Y.; Akita, Y.; Junko, N.; Yatsuga, S.; Povalko, N.; Fukiyama, R.; Ishii, M.; Matsuishi, T. Endothelial dysfunction in melas improved by L-arginine supplementation. Neurology 2006, 66, 1766-1769.
-
(2006)
Neurology
, vol.66
, pp. 1766-1769
-
-
Koga, Y.1
Akita, Y.2
Junko, N.3
Yatsuga, S.4
Povalko, N.5
Fukiyama, R.6
Ishii, M.7
Matsuishi, T.8
-
10
-
-
0037066134
-
Effects of L-arginine on the acute phase of strokes in three patients with melas
-
Koga, Y.; Ishibashi, M.; Ueki, I.; Yatsuga, S.; Fukiyama, R.; Akita, Y.; Matsuishi, T. Effects of L-arginine on the acute phase of strokes in three patients with melas. Neurology 2002, 58, 827-828.
-
(2002)
Neurology
, vol.58
, pp. 827-828
-
-
Koga, Y.1
Ishibashi, M.2
Ueki, I.3
Yatsuga, S.4
Fukiyama, R.5
Akita, Y.6
Matsuishi, T.7
-
11
-
-
13844321746
-
L-arginine improves the symptoms of strokelike episodes in melas
-
Koga, Y.; Akita, Y.; Nishioka, J.; Yatsuga, S.; Povalko, N.; Tanabe, Y.; Fujimoto, S.; Matsuishi, T. L-arginine improves the symptoms of strokelike episodes in melas. Neurology 2005, 64, 710-712.
-
(2005)
Neurology
, vol.64
, pp. 710-712
-
-
Koga, Y.1
Akita, Y.2
Nishioka, J.3
Yatsuga, S.4
Povalko, N.5
Tanabe, Y.6
Fujimoto, S.7
Matsuishi, T.8
-
12
-
-
33847643298
-
MELAS and L-arginine therapy
-
Koga, Y.; Akita, Y.; Nishioka, J.; Yatsuga, S.; Povalko, N.; Katayama, K.; Matsuishi, T. MELAS and L-arginine therapy. Mitochondrion 2007, 7, 133-139.
-
(2007)
Mitochondrion
, vol.7
, pp. 133-139
-
-
Koga, Y.1
Akita, Y.2
Nishioka, J.3
Yatsuga, S.4
Povalko, N.5
Katayama, K.6
Matsuishi, T.7
-
13
-
-
0026573082
-
Defects in mitochondrial protein synthesis and respiratory chain activity segregate with the tRNA(Leu(UUR) mutation associated with mitochondrial myopathy, encephalopathy, lactic acidosis, and strokelike episodes
-
King, M.P.; Koga, Y.; Davidson, M.; Schon, E.A. Defects in mitochondrial protein synthesis and respiratory chain activity segregate with the tRNA(Leu(UUR) mutation associated with mitochondrial myopathy, encephalopathy, lactic acidosis, and strokelike episodes. Mol. Cell. Biol. 1992, 12, 480-490.
-
(1992)
Mol. Cell. Biol.
, vol.12
, pp. 480-490
-
-
King, M.P.1
Koga, Y.2
Davidson, M.3
Schon, E.A.4
-
14
-
-
0032557830
-
Determination of nitrite/nitrate in human biological material by the simple Griess reaction
-
Guevara, I.; Iwanejko, J.; Dembinska-Kiec, A.; Pankiewicz, J.; Wanat, A.; Anna, P.; Golabek, I.; Bartus, S.; Malczewska-Malec, M.; Szczudlik, A. Determination of nitrite/nitrate in human biological material by the simple Griess reaction. Clin. Chim. Acta 1998, 274, 177-188.
-
(1998)
Clin. Chim. Acta
, vol.274
, pp. 177-188
-
-
Guevara, I.1
Iwanejko, J.2
Dembinska-Kiec, A.3
Pankiewicz, J.4
Wanat, A.5
Anna, P.6
Golabek, I.7
Bartus, S.8
Malczewska-Malec, M.9
Szczudlik, A.10
-
15
-
-
84859426945
-
In vivo functional brain imaging and a therapeutic trial of L-arginine in melas patients
-
Yoneda, M.; Ikawa, M.; Arakawa, K.; Kudo, T.; Kimura, H.; Fujibayashi, Y.; Okazawa, H. In vivo functional brain imaging and a therapeutic trial of L-arginine in melas patients. Biochim. Biophys. Acta 2012, 1820, 615-618.
-
(2012)
Biochim. Biophys. Acta
, vol.1820
, pp. 615-618
-
-
Yoneda, M.1
Ikawa, M.2
Arakawa, K.3
Kudo, T.4
Kimura, H.5
Fujibayashi, Y.6
Okazawa, H.7
-
16
-
-
4444325550
-
Beneficial effect of L-arginine for stroke-like episode in MELAS
-
Discussion 480
-
Kubota, M.; Sakakihara, Y.; Mori, M.; Yamagata, T.; Momoi-Yoshida, M. Beneficial effect of L-arginine for stroke-like episode in MELAS. Brain Dev. 2004, 26, 481-483; Discussion 480.
-
(2004)
Brain Dev.
, vol.26
, pp. 481-483
-
-
Kubota, M.1
Sakakihara, Y.2
Mori, M.3
Yamagata, T.4
Momoi-Yoshida, M.5
-
17
-
-
84858700111
-
Restoration of impaired nitric oxide production in melas syndrome with citrulline and arginine supplementation
-
El-Hattab, A.W.; Hsu, J.W.; Emrick, L.T.; Wong, L.J.; Craigen, W.J.; Jahoor, F.; Scaglia, F. Restoration of impaired nitric oxide production in melas syndrome with citrulline and arginine supplementation. Mol. Genet. Metab. 2012, 105, 607-614.
-
(2012)
Mol. Genet. Metab.
, vol.105
, pp. 607-614
-
-
El-Hattab, A.W.1
Hsu, J.W.2
Emrick, L.T.3
Wong, L.J.4
Craigen, W.J.5
Jahoor, F.6
Scaglia, F.7
-
18
-
-
77955288655
-
MELAS and L-arginine therapy: Pathophysiology of stroke-like episodes
-
Koga, Y.; Povalko, N.; Nishioka, J.; Katayama, K.; Kakimoto, N.; Matsuishi, T. MELAS and L-arginine therapy: Pathophysiology of stroke-like episodes. Ann. N. Y. Acad. Sci. 2010, 1201, 104-110.
-
(2010)
Ann. N.Y. Acad. Sci.
, vol.1201
, pp. 104-110
-
-
Koga, Y.1
Povalko, N.2
Nishioka, J.3
Katayama, K.4
Kakimoto, N.5
Matsuishi, T.6
-
19
-
-
84867895466
-
Citrulline and arginine utility in treating nitric oxide deficiency in mitochondrial disorders
-
El-Hattab, A.W.; Emrick, L.T.; Craigen, W.J.; Scaglia, F. Citrulline and arginine utility in treating nitric oxide deficiency in mitochondrial disorders. Mol. Genet. Metab. 2012, 107, 247-252.
-
(2012)
Mol. Genet. Metab.
, vol.107
, pp. 247-252
-
-
El-Hattab, A.W.1
Emrick, L.T.2
Craigen, W.J.3
Scaglia, F.4
-
20
-
-
14844303949
-
Hypocitrullinemia in patients with melas: An insight into the "melas paradox"
-
Naini, A.; Kaufmann, P.; Shanske, S.; Engelstad, K.; de Vivo, D.C.; Schon, E.A. Hypocitrullinemia in patients with melas: An insight into the "melas paradox". J. Neurol. Sci. 2005, 229-230, 187-193.
-
(2005)
J. Neurol. Sci.
-
-
Naini, A.1
Kaufmann, P.2
Shanske, S.3
Engelstad, K.4
de Vivo, D.C.5
Schon, E.A.6
-
21
-
-
0030567976
-
Localization of nitric oxide synthase in human skeletal muscle
-
Frandsen, U.; Lopez-Figueroa, M.; Hellsten, Y. Localization of nitric oxide synthase in human skeletal muscle. Biochem. Biophys. Res. Commun. 1996, 227, 88-93.
-
(1996)
Biochem. Biophys. Res. Commun.
, vol.227
, pp. 88-93
-
-
Frandsen, U.1
Lopez-Figueroa, M.2
Hellsten, Y.3
-
22
-
-
0033912406
-
Skeletal muscle fibres show NADPH diaphorase activity associated with mitochondria, the sarcoplasmic reticulum and the NOS-1-containing sarcolemma
-
Planitzer, G.; Baum, O.; Gossrau, R. Skeletal muscle fibres show NADPH diaphorase activity associated with mitochondria, the sarcoplasmic reticulum and the NOS-1-containing sarcolemma. Histochem. J. 2000, 32, 303-312.
-
(2000)
Histochem. J.
, vol.32
, pp. 303-312
-
-
Planitzer, G.1
Baum, O.2
Gossrau, R.3
-
23
-
-
34250159850
-
The role of nitric oxide in muscle fibers with oxidative phosphorylation defects
-
Tengan, C.H.; Kiyomoto, B.H.; Godinho, R.O.; Gamba, J.; Neves, A.C.; Schmidt, B.; Oliveira, A.S.; Gabbai, A.A. The role of nitric oxide in muscle fibers with oxidative phosphorylation defects. Biochem. Biophys. Res. Commun. 2007, 359, 771-777.
-
(2007)
Biochem. Biophys. Res. Commun.
, vol.359
, pp. 771-777
-
-
Tengan, C.H.1
Kiyomoto, B.H.2
Godinho, R.O.3
Gamba, J.4
Neves, A.C.5
Schmidt, B.6
Oliveira, A.S.7
Gabbai, A.A.8
-
24
-
-
79953322206
-
Increased protein nitration in mitochondrial diseases: Evidence for vessel wall involvement
-
M110.002964
-
Vattemi, G.; Mechref, Y.; Marini, M.; Tonin, P.; Minuz, P.; Grigoli, L.; Guglielmi, V.; Klouckova, I.; Chiamulera, C.; Meneguzzi, A.; et al. Increased protein nitration in mitochondrial diseases: Evidence for vessel wall involvement. Mol. Cell. Proteomics 2011, 10, M110.002964.
-
(2011)
Mol. Cell. Proteomics
, vol.10
-
-
Vattemi, G.1
Mechref, Y.2
Marini, M.3
Tonin, P.4
Minuz, P.5
Grigoli, L.6
Guglielmi, V.7
Klouckova, I.8
Chiamulera, C.9
Meneguzzi, A.10
-
25
-
-
49949087968
-
New indications and controversies in arginine therapy
-
Coman, D.; Yaplito-Lee, J.; Boneh, A. New indications and controversies in arginine therapy. Clin. Nutr. 2008, 27, 489-496.
-
(2008)
Clin. Nutr.
, vol.27
, pp. 489-496
-
-
Coman, D.1
Yaplito-Lee, J.2
Boneh, A.3
-
26
-
-
78649711229
-
Abnormal myocardial energy-production state in mitochondrial cardiomyopathy and acute response to L-arginine infusion. C-11 acetate kinetics revealed by positron emission tomography
-
Arakawa, K.; Kudo, T.; Ikawa, M.; Morikawa, N.; Kawai, Y.; Sahashi, K.; Lee, J.D.; Kuriyama, M.; Miyamori, I.; Okazawa, H.; et al. Abnormal myocardial energy-production state in mitochondrial cardiomyopathy and acute response to L-arginine infusion. C-11 acetate kinetics revealed by positron emission tomography. Circ. J. 2010, 74, 2702-2711.
-
(2010)
Circ. J.
, vol.74
, pp. 2702-2711
-
-
Arakawa, K.1
Kudo, T.2
Ikawa, M.3
Morikawa, N.4
Kawai, Y.5
Sahashi, K.6
Lee, J.D.7
Kuriyama, M.8
Miyamori, I.9
Okazawa, H.10
-
27
-
-
84859034463
-
Metabolically induced heteroplasmy shifting and L-arginine treatment reduce the energetic defect in a neuronal-like model of melas
-
Desquiret-Dumas, V.; Gueguen, N.; Barth, M.; Chevrollier, A.; Hancock, S.; Wallace, D.C.; Amati-Bonneau, P.; Henrion, D.; Bonneau, D.; Reynier, P.; et al. Metabolically induced heteroplasmy shifting and L-arginine treatment reduce the energetic defect in a neuronal-like model of melas. Biochim. Biophys. Acta 2012, 1822, 1019-1029.
-
(2012)
Biochim. Biophys. Acta
, vol.1822
, pp. 1019-1029
-
-
Desquiret-Dumas, V.1
Gueguen, N.2
Barth, M.3
Chevrollier, A.4
Hancock, S.5
Wallace, D.C.6
Amati-Bonneau, P.7
Henrion, D.8
Bonneau, D.9
Reynier, P.10
-
30
-
-
33746841367
-
Nitric oxide and mitochondrial biogenesis
-
Nisoli, E.; Carruba, M.O. Nitric oxide and mitochondrial biogenesis. J. Cell. Sci. 2006, 119, 2855-2862.
-
(2006)
J. Cell. Sci.
, vol.119
, pp. 2855-2862
-
-
Nisoli, E.1
Carruba, M.O.2
-
31
-
-
0035139227
-
Physiology of nitric oxide in skeletal muscle
-
Stamler, J.S.; Meissner, G. Physiology of nitric oxide in skeletal muscle. Physiol. Rev. 2001, 81, 209-237.
-
(2001)
Physiol. Rev.
, vol.81
, pp. 209-237
-
-
Stamler, J.S.1
Meissner, G.2
-
32
-
-
0034082985
-
Regulation of mitochondrial respiration by oxygen and nitric oxide
-
Boveris, A.; Costa, L.E.; Poderoso, J.J.; Carreras, M.C.; Cadenas, E. Regulation of mitochondrial respiration by oxygen and nitric oxide. Ann. N. Y. Acad. Sci. 2000, 899, 121-135.
-
(2000)
Ann. N.Y. Acad. Sci.
, vol.899
, pp. 121-135
-
-
Boveris, A.1
Costa, L.E.2
Poderoso, J.J.3
Carreras, M.C.4
Cadenas, E.5
-
33
-
-
84872188859
-
Complex I spectrophotometric assay in cultured cells: Detailed analysis of key factors
-
doi:10.1016/j.ab.2012.12.002
-
Oliveira, K.K.; Kiyomoto, B.H.; Tengan, C.H. Complex I spectrophotometric assay in cultured cells: Detailed analysis of key factors. Anal. Biochem. 2012, doi:10.1016/j.ab.2012.12.002.
-
(2012)
Anal. Biochem.
-
-
Oliveira, K.K.1
Kiyomoto, B.H.2
Tengan, C.H.3
-
34
-
-
70249133648
-
Development and implementation of standardized respiratory chain spectrophotometric assays for clinical diagnosis
-
Medja, F.; Allouche, S.; Frachon, P.; Jardel, C.; Malgat, M.; Mousson de Camaret, B.; Slama, A.; Lunardi, J.; Mazat, J.P.; Lombes, A. Development and implementation of standardized respiratory chain spectrophotometric assays for clinical diagnosis. Mitochondrion 2009, 9, 331-339.
-
(2009)
Mitochondrion
, vol.9
, pp. 331-339
-
-
Medja, F.1
Allouche, S.2
Frachon, P.3
Jardel, C.4
Malgat, M.5
Mousson de Camaret, B.6
Slama, A.7
Lunardi, J.8
Mazat, J.P.9
Lombes, A.10
-
35
-
-
0029790507
-
Altered mitochondrial function in fibroblasts containing MELAS or MERRF mitochondrial DNA mutations
-
James, A.M.; Wei, Y.H.; Pang, C.Y.; Murphy, M.P. Altered mitochondrial function in fibroblasts containing MELAS or MERRF mitochondrial DNA mutations. Biochem. J. 1996, 318, 401-407.
-
(1996)
Biochem. J.
, vol.318
, pp. 401-407
-
-
James, A.M.1
Wei, Y.H.2
Pang, C.Y.3
Murphy, M.P.4
-
36
-
-
75749093396
-
Evaluation of the mitochondrial respiratory chain and oxidative phosphorylation system using polarography and spectrophotometric enzyme assays
-
doi:10.1002/0471142905.hg1903s63
-
Barrientos, A.; Fontanesi, F.; Diaz, F. Evaluation of the mitochondrial respiratory chain and oxidative phosphorylation system using polarography and spectrophotometric enzyme assays. Curr. Protoc. Hum. Genet. 2009, doi:10.1002/0471142905.hg1903s63.
-
(2009)
Curr. Protoc. Hum. Genet.
-
-
Barrientos, A.1
Fontanesi, F.2
Diaz, F.3
-
37
-
-
63449114461
-
Chapter 9 reliable assay for measuring complex I activity in human blood lymphocytes and skin fibroblasts
-
De Wit, L.E.; Sluiter, W. Chapter 9 reliable assay for measuring complex I activity in human blood lymphocytes and skin fibroblasts. Meth. Enzymology 2009, 456, 169-181.
-
(2009)
Meth. Enzymology
, vol.456
, pp. 169-181
-
-
de Wit, L.E.1
Sluiter, W.2
-
38
-
-
0036024973
-
In vivo and in organello assessment of oxphos activities
-
Barrientos, A. In vivo and in organello assessment of oxphos activities. Methods 2002, 26, 307-316.
-
(2002)
Methods
, vol.26
, pp. 307-316
-
-
Barrientos, A.1
-
39
-
-
0034213229
-
A spectrophotometric method for the direct detection and quantitation of nitric oxide, nitrite, and nitrate in cell culture media
-
Ridnour, L.A.; Sim, J.E.; Hayward, M.A.; Wink, D.A.; Martin, S.M.; Buettner, G.R.; Spitz, D.R. A spectrophotometric method for the direct detection and quantitation of nitric oxide, nitrite, and nitrate in cell culture media. Anal. Biochem. 2000, 281, 223-229.
-
(2000)
Anal. Biochem.
, vol.281
, pp. 223-229
-
-
Ridnour, L.A.1
Sim, J.E.2
Hayward, M.A.3
Wink, D.A.4
Martin, S.M.5
Buettner, G.R.6
Spitz, D.R.7
-
40
-
-
0035709008
-
A rapid, simple spectrophotometric method for simultaneous detection of nitrate and nitrite
-
Miranda, K.M.; Espey, M.G.; Wink, D.A. A rapid, simple spectrophotometric method for simultaneous detection of nitrate and nitrite. Nitric Oxide 2001, 5, 62-71.
-
(2001)
Nitric Oxide
, vol.5
, pp. 62-71
-
-
Miranda, K.M.1
Espey, M.G.2
Wink, D.A.3
-
41
-
-
0032109160
-
Detection and imaging of nitric oxide with novel fluorescent indicators: Diaminofluoresceins
-
Kojima, H.; Nakatsubo, N.; Kikuchi, K.; Kawahara, S.; Kirino, Y.; Nagoshi, H.; Hirata, Y.; Nagano, T. Detection and imaging of nitric oxide with novel fluorescent indicators: Diaminofluoresceins. Anal. Chem. 1998, 70, 2446-2453.
-
(1998)
Anal. Chem.
, vol.70
, pp. 2446-2453
-
-
Kojima, H.1
Nakatsubo, N.2
Kikuchi, K.3
Kawahara, S.4
Kirino, Y.5
Nagoshi, H.6
Hirata, Y.7
Nagano, T.8
-
42
-
-
0036479238
-
Selective nitration of histone tyrosine residues in vivo in mutatect tumors
-
Haqqani, A.S.; Kelly, J.F.; Birnboim, H.C. Selective nitration of histone tyrosine residues in vivo in mutatect tumors. J. Biol. Chem. 2002, 277, 3614-3621.
-
(2002)
J. Biol. Chem.
, vol.277
, pp. 3614-3621
-
-
Haqqani, A.S.1
Kelly, J.F.2
Birnboim, H.C.3
|