Hypocitrullinemia in patients with MELAS: An insight into the "MELAS paradox"

Journal of the Neurological Sciences

Volumn 229-230, Issue , 2005, Pages 187-193

  Naini, Ali ^a   Kaufmann, Petra ^a   Shanske, Sara ^a   Engelstad, Kristin ^a   De Vivo, Darryl C ^a   Schon, Eric A ^a  

^a New York Presbyterian Columbia University Medical Center   (United States)

Author keywords

Arginine; Citrulline; Cytochrome c oxidase; Mitochondria; Nitric oxide

Indexed keywords

ARGININE; CITRULLINE; DELTA 1 PYRROLINE CARBOXYLATE SYNTHASE; ESSENTIAL AMINO ACID; NITRIC OXIDE; NITRIC OXIDE SYNTHASE; SYNTHETASE; UNCLASSIFIED DRUG;

ADULT; AMINO ACID BLOOD LEVEL; AMINO ACID SYNTHESIS; BLOOD ANALYSIS; CELL STRUCTURE; CELLULAR DISTRIBUTION; CITRULLINEMIA; CONFERENCE PAPER; CONTROLLED STUDY; CORRELATION ANALYSIS; DISORDERS OF MITOCHONDRIAL FUNCTIONS; ENDOTHELIUM CELL; EXTRACHROMOSOMAL INHERITANCE; FEMALE; HETEROPLASMY; HOMEOSTASIS; HUMAN; HYPOTHESIS; MALE; MELAS SYNDROME; PRIORITY JOURNAL; PROTEIN EXPRESSION; RESPIRATORY CHAIN; SMALL INTESTINE;

EID: 14844303949     PISSN: 0022510X     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.jns.2004.11.026     Document Type: Conference Paper

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