The RNA-binding motif 45 (RBM45) protein accumulates in inclusion bodies in amyotrophic lateral sclerosis (ALS) and frontotemporal lobar degeneration with TDP-43 inclusions (FTLD-TDP) patients

Acta Neuropathologica

Volumn 124, Issue 5, 2012, Pages 717-732

  Collins, Mahlon ^a   Riascos, David ^d   Kovalik, Tina ^d   An, Jiyan ^d   Krupa, Kelly ^a   Krupa, Kristin ^a   Hood, Brian L ^b   Conrads, Thomas P ^b   Renton, Alan E ^c   Traynor, Bryan J ^c   Bowser, Robert ^a,d  

^a UNIVERSITY OF PITTSBURGH SCHOOL OF MEDICINE   (United States)

^b BETTY AND GUY BEATTY CENTER FOR INTEGRATED RESEARCH   (United States)

^c NATIONAL INSTITUTES OF HEALTH   (United States)

^d BARROW NEUROLOGICAL INSTITUTE   (United States)

Author keywords

Amyotrophic lateral sclerosis; C9ORF72; Frontotemporal lobar degeneration; RBM45; RNA binding protein; TDP 43

Indexed keywords

FUSED IN SARCOMA PROTEIN; RNA BINDING MOTIF 45 PROTEIN; RNA BINDING PROTEIN; TAR DNA BINDING PROTEIN; UBIQUITIN; UNCLASSIFIED DRUG;

ADULT; AGED; ALZHEIMER DISEASE; AMINO ACID SEQUENCE; AMYOTROPHIC LATERAL SCLEROSIS; ARTICLE; BRAIN NERVE CELL; C9ORF72 GENE; CELL INCLUSION; CEREBROSPINAL FLUID ANALYSIS; CEREBROSPINAL FLUID LEVEL; CLINICAL ARTICLE; CONFOCAL MICROSCOPY; CONTROLLED STUDY; DENTATE GYRUS; DNA STRUCTURE; FEMALE; FRONTOTEMPORAL DEMENTIA; GENE; GLIA CELL; HEXANUCLEOTIDE REPEAT EXPANSION; HIPPOCAMPUS; HUMAN; HUMAN TISSUE; IMMUNOBLOTTING; IMMUNOHISTOCHEMISTRY; LIQUID CHROMATOGRAPHY; MALE; NUCLEOTIDE SEQUENCE; PRIORITY JOURNAL; PROTEIN LOCALIZATION; SPINAL CORD; SPINAL CORD MOTONEURON; TANDEM MASS SPECTROMETRY; TISSUE LEVEL;

ADULT; AGED; AGED, 80 AND OVER; AMYOTROPHIC LATERAL SCLEROSIS; BRAIN; CHROMATOGRAPHY, LIQUID; DNA-BINDING PROTEINS; FEMALE; FRONTOTEMPORAL LOBAR DEGENERATION; GENE EXPRESSION REGULATION; HUMANS; INCLUSION BODIES; MALE; MIDDLE AGED; MUTATION; NERVE TISSUE PROTEINS; NEURONS; PROTEINS; RNA-BINDING PROTEINS; SPINAL CORD; TANDEM MASS SPECTROMETRY;

EID: 84870993605     PISSN: 00016322     EISSN: 14320533     Source Type: Journal    
DOI: 10.1007/s00401-012-1045-x     Document Type: Article

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