Defective surfactant secretion in a mouse model of Hermansky-Pudlak syndrome

American Journal of Respiratory Cell and Molecular Biology

Volumn 33, Issue 1, 2005, Pages 14-21

  Guttentag, Susan H ^a   Akhtar, Amana ^b   Tao, Jian Qin ^b   Atochina, Elena ^b   Rusiniak, Michael E ^b   Swank, Richard T ^b   Bates, Sandra R ^b  

^a CHILDREN S HOSPITAL OF PHILADELPHIA   (United States)

^b NONE

Author keywords

Alveolar type II cell; Hermansky Pudlak syndrome; Lamellar body; Secretion; Surfactant

Indexed keywords

SURFACTANT ASSOCIATED PROTEIN; SURFACTANT PROTEIN B; SURFACTANT PROTEIN C; SURFACTANT PROTEIN D;

ANIMAL EXPERIMENT; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; EXPERIMENTAL MODEL; FEMALE; LAMELLAR BODY; MALE; MOUSE; NONHUMAN; OCULAR ALBINISM; SURFACE TENSION;

ANIMALS; BLOTTING, WESTERN; BRONCHOALVEOLAR LAVAGE; CAPILLARIES; DENSITOMETRY; DISEASE MODELS, ANIMAL; HERMANSKI-PUDLAK SYNDROME; HUMANS; IMMUNOBLOTTING; MALE; MICE; MICE, INBRED C57BL; MICE, TRANSGENIC; MICROSCOPY, FLUORESCENCE; PHOSPHOLIPIDS; PULMONARY SURFACTANT-ASSOCIATED PROTEIN A; PULMONARY SURFACTANT-ASSOCIATED PROTEIN B; PULMONARY SURFACTANT-ASSOCIATED PROTEIN C; PULMONARY SURFACTANT-ASSOCIATED PROTEIN D; REVERSE TRANSCRIPTASE POLYMERASE CHAIN REACTION; RNA, MESSENGER; SURFACE-ACTIVE AGENTS; TIME FACTORS;

ANIMALIA;

EID: 21844441925     PISSN: 10441549     EISSN: None     Source Type: Journal    
DOI: 10.1165/rcmb.2004-0293OC     Document Type: Article

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