BAG-1 stabilizes mutant F508del-CFTR in a ubiquitin-like-domain-dependent manner

Cellular Physiology and Biochemistry

Volumn 30, Issue 5, 2012, Pages 1120-1133

  Mendes, Filipa ^a,b,c   Farinha, Carlos M ^b   Felício, Verónica ^b   Alves, Paulo C ^a   Vieira, Isabel ^a   Amaral, Margarida D ^a,b  

^a NATIONAL INSTITUTE OF HEALTH DR RICARDO JORGE   (Portugal)

^b UNIVERSITY OF LISBON   (Portugal)

^c INSTITUTO SUPERIOR TÉCNICO   (Portugal)

Author keywords

BAG 1; CFTR; Cystic Fibrosis; ERAD; Hsp70; Ubiquitin

Indexed keywords

BAG 1 PROTEIN; CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR; HEAT SHOCK COGNATE PROTEIN 70; MUTANT PROTEIN; PROTEASOME INHIBITOR; UBIQUITIN;

ANIMAL CELL; ARTICLE; CONTROLLED STUDY; GENE OVEREXPRESSION; IN VIVO STUDY; NONHUMAN; PRIORITY JOURNAL; PROTEIN DOMAIN; PROTEIN FUNCTION; PROTEIN METABOLISM; PROTEIN PROCESSING; PROTEIN STABILITY; WILD TYPE;

ANIMALS; CHO CELLS; CRICETINAE; CRICETULUS; CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR; DNA-BINDING PROTEINS; HSP70 HEAT-SHOCK PROTEINS; MOLECULAR SEQUENCE DATA; MUTANT PROTEINS; MUTATION; PROTEIN BINDING; PROTEIN STRUCTURE, TERTIARY; TRANSCRIPTION FACTORS; UBIQUITIN; UBIQUITINATION;

EID: 84869203984     PISSN: 10158987     EISSN: 14219778     Source Type: Journal    
DOI: 10.1159/000343303     Document Type: Article

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