Lymphangioleiomyomatosis: New concepts in pathogenesis, diagnosis, and treatment

Seminars in Respiratory and Critical Care Medicine

Volumn 33, Issue 5, 2012, Pages 486-497

  Meraj, Riffat ^a   Wikenheiser Brokamp, Kathryn A ^a,b   Young, Lisa R ^c   McCormack, Francis X ^a  

^a UNIVERSITY OF CINCINNATI COLLEGE OF MEDICINE   (United States)

^b CINCINNATI CHILDREN'S HOSPITAL MEDICAL CENTER   (United States)

^c VANDERBILT UNIVERSITY   (United States)

Author keywords

angiomyolipomas; lymphangioleiomyomatosis; lymphangiomyomas; tuberous sclerosis

Indexed keywords

CARBON MONOXIDE; MAMMALIAN TARGET OF RAPAMYCIN; MONOCLONAL ANTIBODY HMB 45; PLACEBO; PODOPLANIN; RAPAMYCIN; TUBERIN;

AIRWAY REMODELING; ANGIOMYOLIPOMA; ARTICLE; AUTOPHAGY; BRONCHIOLITIS; CANCER DIAGNOSIS; CANCER PATIENT; CANCER SCREENING; CELL ISOLATION; CENTRIFUGATION; CHYLE; COMPUTER ASSISTED TOMOGRAPHY; CYTODIAGNOSIS; DIFFERENTIAL DIAGNOSIS; DRUG WITHDRAWAL; DYSPNEA; FORCED EXPIRATORY VOLUME; GENE MUTATION; GENETIC LINKAGE; GERM LINE; HISTIOCYTOSIS; HUMAN; IMMUNOCYTOCHEMISTRY; LUNG ARTERY PRESSURE; LUNG BIOPSY; LUNG CONGESTION; LUNG CYST; LUNG DIFFUSION CAPACITY; LUNG PARENCHYMA; LUNG TRANSPLANTATION; LYMPHANGIOGENESIS; LYMPHANGIOLEIOMYOMATOSIS; LYMPHANGIOMYOMA; MALIGNANT NEOPLASTIC DISEASE; MELANOGENESIS; MOLECULARLY TARGETED THERAPY; MORBIDITY; MOSAICISM; MULTIPLE ENDOCRINE NEOPLASIA; NON INVASIVE PROCEDURE; NUCLEAR MAGNETIC RESONANCE IMAGING; PATHOGENESIS; PEROPERATIVE COMPLICATION; PLEURECTOMY; PLEURISY; PLEURODESIS; PNEUMOTHORAX; PRIORITY JOURNAL; PULMONARY HYPERTENSION; QUALITY OF LIFE; RANDOMIZED CONTROLLED TRIAL (TOPIC); RECURRENT DISEASE; SERODIAGNOSIS; SMOKING CESSATION; SMOOTH MUSCLE FIBER; TRANSBRONCHIAL BIOPSY; TUBEROUS SCLEROSIS; TUMOR EMBOLISM; UNSPECIFIED SIDE EFFECT; VIDEO ASSISTED THORACOSCOPIC SURGERY;

DISEASE PROGRESSION; DYSPNEA; FEMALE; HUMANS; LYMPHANGIOLEIOMYOMATOSIS; MALE; MOLECULAR TARGETED THERAPY; MUTATION; PLEURAL EFFUSION; PNEUMOTHORAX; RECURRENCE; SEX FACTORS; TUBEROUS SCLEROSIS;

EID: 84866504036     PISSN: 10693424     EISSN: 10989048     Source Type: Journal    
DOI: 10.1055/s-0032-1325159     Document Type: Article

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