Is sirolimus a therapeutic option for patients with progressive pulmonary lymphangioleiomyomatosis?

Respiratory Research

Volumn 12, Issue 1, 2011, Pages

  Neurohr, Claus ^a   Hoffmann, Anna L ^a   Huppmann, Patrick ^a   Herrera, Vivian A ^a   Ihle, Franziska ^a   Leuschner, Stefan ^a   von Wulffen, Werner ^a   Meis, Tobias ^a   Baezner, Carlos ^a   Leuchte, Hanno ^a   Baumgartner, Rainer ^a   Zimmermann, Gregor ^a   Behr, Juergen ^a  

^a LUDWIG MAXIMILIANS UNIVERSITY   (Germany)

Author keywords

[No Author keywords available]

Indexed keywords

RAPAMYCIN; RESPIRATORY TRACT AGENT;

ADULT; APHTHOUS STOMATITIS; ARTICLE; BLEEDING; CLINICAL ARTICLE; DISEASE COURSE; DRUG FATALITY; DRUG WITHDRAWAL; FEMALE; FEVER; FOLLOW UP; FORCED EXPIRATORY VOLUME; FORCED VITAL CAPACITY; FUNCTIONAL ASSESSMENT; HUMAN; KIDNEY DYSFUNCTION; LEUKOPENIA; LOWER RESPIRATORY TRACT INFECTION; LUNG FUNCTION TEST; LYMPHANGIOLEIOMYOMATOSIS; OBSERVATIONAL STUDY; PERIPHERAL EDEMA; PLEURA EFFUSION; PNEUMONIA; PNEUMOTHORAX; SIX MINUTE WALK DISTANCE; TREATMENT OUTCOME; TREATMENT WITHDRAWAL; CHEMICALLY INDUCED DISORDER; CONVALESCENCE; DRUG EFFECT; EXERCISE TEST; GERMANY; LUNG; LUNG TUMOR; MIDDLE AGED; PATHOPHYSIOLOGY; RESPIRATORY TRACT INFECTION; TIME; VITAL CAPACITY;

ADULT; DISEASE PROGRESSION; EXERCISE TEST; FEMALE; FORCED EXPIRATORY VOLUME; GERMANY; HUMANS; LUNG; LUNG NEOPLASMS; LYMPHANGIOLEIOMYOMATOSIS; MIDDLE AGED; PNEUMONIA; RECOVERY OF FUNCTION; RESPIRATORY FUNCTION TESTS; RESPIRATORY SYSTEM AGENTS; RESPIRATORY TRACT INFECTIONS; SIROLIMUS; TIME FACTORS; TREATMENT OUTCOME; VITAL CAPACITY;

EID: 79956189227     PISSN: 14659921     EISSN: 1465993X     Source Type: Journal    
DOI: 10.1186/1465-9921-12-66     Document Type: Article

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