Changes in mitochondrial glutathione levels and protein thiol oxidation in Δyfh1 yeast cells and the lymphoblasts of patients with Friedreich's ataxia

Biochimica et Biophysica Acta - Molecular Basis of Disease

Volumn 1822, Issue 2, 2012, Pages 212-225

  Bulteau, A L ^b   Planamente, S ^a   Jornea, L ^b   Dur, A ^b   Lesuisse, E ^a   Camadro, J M ^a   Auchere F ^a  

^a INSTITUT JACQUES MONOD   (France)

^b PITIÉ SALPÊTRIÈRE HOSPITAL   (France)

Author keywords

Friedreich's ataxia; Glutathione; Iron; Mitochondrion; Protein glutathionylation; Thiol oxidation

Indexed keywords

FRATAXIN; GLUTATHIONE; GLUTATHIONE DISULFIDE; IRON; OXOGLUTARATE DEHYDROGENASE; PROTEASOME; PROTEINASE; THIOL;

ARTICLE; CELLULAR DISTRIBUTION; ENZYME ACTIVITY; FRIEDREICH ATAXIA; HUMAN; HUMAN CELL; LYMPHOBLAST; MITOCHONDRIAL RESPIRATION; NONHUMAN; OXIDATION; OXIDATIVE STRESS; PRIORITY JOURNAL; RESPIRATORY CHAIN; SIGNAL TRANSDUCTION; YEAST CELL;

ANTIOXIDANTS; FRIEDREICH ATAXIA; GLUTATHIONE; GLUTATHIONE DISULFIDE; HOMEOSTASIS; HUMANS; IRON; IRON-BINDING PROTEINS; LYMPHOCYTES; MITOCHONDRIA; MITOCHONDRIAL PROTEINS; OXIDATION-REDUCTION; OXIDATIVE STRESS; PROTEASE LA; PROTEASOME ENDOPEPTIDASE COMPLEX; PROTEIN BINDING; SACCHAROMYCES CEREVISIAE; SULFHYDRYL COMPOUNDS;

EID: 83255165402     PISSN: 09254439     EISSN: 1879260X     Source Type: Journal    
DOI: 10.1016/j.bbadis.2011.11.003     Document Type: Article

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