Lysosomal vitamin E accumulation in Niemann-Pick type C disease

Biochimica et Biophysica Acta - Molecular Basis of Disease

Volumn 1822, Issue 2, 2012, Pages 150-160

  Yévenes, Luz Fernanda ^a,b   Klein, Andrés ^b   Castro, Juan Francisco ^b   Marín, Tamara ^b   Leal, Nancy ^a   Leighton, Federico ^a   Alvarez, Alejandra R ^a   Zanlungo, Silvana ^b,c  

^a PONTIFICIA UNIVERSIDAD CATÓLICA DE CHILE   (Chile)

^b PONTIFICIA UNIVERSIDAD CATÓLICA DE CHILE   (Chile)

^c FONDAP Center for Genome Regulation   (Chile)

Author keywords

Cholesterol; Lysosomes; Niemann Pick C; Vitamin E

Indexed keywords

3BETA (2 DIETHYLAMINOETHOXY)ANDROST 5 EN 17 ONE; ALPHA TOCOPHEROL; ALPHA TOCOPHEROL TRANSFER PROTEIN; ALPHA TOCOPHEROL TRANSPORTER; CARRIER PROTEIN; CHOLESTEROL; MESSENGER RNA; UNCLASSIFIED DRUG;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BIOAVAILABILITY; BRAIN LEVEL; BRAIN NERVE CELL; CEREBELLUM; CONFOCAL MICROSCOPY; CONTROLLED STUDY; EMBRYO; ENDOCYTOSIS; GENE EXPRESSION; IMMUNOFLUORESCENCE MICROSCOPY; INTRACELLULAR TRANSPORT; LIVER; LIVER LEVEL; LYSOSOME; MOUSE; NIEMANN PICK DISEASE; NONHUMAN; PRIORITY JOURNAL; VITAMIN METABOLISM;

ANIMALS; ANTIOXIDANTS; BIOLOGICAL AVAILABILITY; BIOLOGICAL TRANSPORT; CELLS, CULTURED; CEREBELLUM; CHOLESTEROL; ENDOCYTOSIS; HIPPOCAMPUS; LIVER; LYSOSOMES; MALE; MICE; MICE, INBRED BALB C; NEURONS; NIEMANN-PICK DISEASE, TYPE C; PROTEINS; RATS; RATS, SPRAGUE-DAWLEY; VITAMIN E;

MUS;

EID: 83155178547     PISSN: 09254439     EISSN: 1879260X     Source Type: Journal    
DOI: 10.1016/j.bbadis.2011.11.009     Document Type: Article

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