NPC2, the protein deficient in Niemann-Pick C2 disease, consists of multiple glycoforms that bind a variety of sterols

Journal of Biological Chemistry

Volumn 281, Issue 48, 2006, Pages 36710-36723

  Liou, Heng Ling ^a,c   Dixit, Sayali S ^a,c   Xu, Sujuan ^a,c   Tint, G Stephen ^d   Stock, Ann M ^a,b,c   Lobel, Peter ^a,c  

^a RUTGERS UNIVERSITY   (United States)

^b HOWARD HUGHES MEDICAL INSTITUTE   (United States)

^c RUTGERS ROBERT WOOD JOHNSON MEDICAL SCHOOL   (United States)

^d VETERANS AFFAIRS MEDICAL CENTER   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

GLYCOFORMS; NIEMANN-PICK C; STEROLS;

CHOLESTEROL; GENETIC ENGINEERING; MASS SPECTROMETRY; PROTEINS;

DISEASES;

ASPARAGINE; GLYCOPROTEIN; OLIGOSACCHARIDE; PROTEIN NPC2; STEROL; UNCLASSIFIED DRUG;

ANIMAL CELL; ARTICLE; CHROMATOGRAPHY; CONTROLLED STUDY; FIBROBLAST; GLYCOSYLATION; MASS SPECTROMETRY; NIEMANN PICK DISEASE; NONHUMAN; PRIORITY JOURNAL; PROTEIN DEFICIENCY; PROTEIN FUNCTION; PROTEIN PURIFICATION; PROTEIN STRUCTURE;

ANIMALS; BIOLOGICAL TRANSPORT; BRAIN; CARRIER PROTEINS; CHOLESTEROL; FIBROBLASTS; GLYCOPROTEINS; GLYCOSYLATION; HUMANS; LIPIDS; LIVER; MICE; NIEMANN-PICK DISEASES; RECOMBINANT PROTEINS; STEROLS;

EID: 33845994402     PISSN: 00219258     EISSN: 1083351X     Source Type: Journal    
DOI: 10.1074/jbc.M608743200     Document Type: Article

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