Abnormal nuclear envelope in the cerebellar Purkinje cells and impaired motor learning in DYT11 myoclonus-dystonia mouse models

Behavioural Brain Research

Volumn 227, Issue 1, 2012, Pages 12-20

  Yokoi, Fumiaki ^a   Dang, Mai T ^b   Yang, Guang ^c   Li, JinDong ^c   Doroodchi, Atbin ^d   Zhou, Tong ^c   Li, Yuqing ^a  

^a UNIVERSITY OF FLORIDA COLLEGE OF MEDICINE   (United States)

^b HOSPITAL OF THE UNIVERSITY OF PENNSYLVANIA   (United States)

^c University of Alabama at Birmingham   (United States)

^d UNIVERSITY OF ALABAMA AT BIRMINGHAM   (United States)

Author keywords

E open Sarcoglycan; Motor learning; Myoclonus dystonia; Nuclear envelope; Purkinje cell; Sgce

Indexed keywords

EPSILON SARCOGLYCAN;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BEAM WALKING TEST; BRAIN REGION; CELL NUCLEUS MEMBRANE; CONTROLLED STUDY; EXPERIMENTAL TEST; FEMALE; GENE SILENCING; HETEROZYGOTE; LEARNING DISORDER; MALE; MOTOR COORDINATION; MOTOR LEARNING DISORDER; MOUSE; MYOCLONUS; MYOCLONUS DYSTONIA; NONHUMAN; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN FUNCTION; PURKINJE CELL; SGCE GENE; TRANSMISSION ELECTRON MICROSCOPY;

ANIMALS; CEREBELLUM; DISEASE MODELS, ANIMAL; DYSTONIA MUSCULORUM DEFORMANS; DYSTONIC DISORDERS; EXPLORATORY BEHAVIOR; EXTRACELLULAR MATRIX PROTEINS; LEARNING DISORDERS; LOCOMOTION; MICE; MICE, INBRED C57BL; MICE, KNOCKOUT; MICROSCOPY, ELECTRON, TRANSMISSION; MOTOR ACTIVITY; NUCLEAR ENVELOPE; POSTURE; PROTEIN-LYSINE 6-OXIDASE; PURKINJE CELLS; ROTAROD PERFORMANCE TEST; SARCOGLYCANS; STEREOTYPED BEHAVIOR;

EID: 81055155485     PISSN: 01664328     EISSN: 18727549     Source Type: Journal    
DOI: 10.1016/j.bbr.2011.10.024     Document Type: Article

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