Dimerization of the DYT6 dystonia protein, THAP1, requires residues within the coiled-coil domain

Journal of Neurochemistry

Volumn 118, Issue 6, 2011, Pages 1087-1100

  Sengel, Cem ^a   Gavarini, Sophie ^b   Sharma, Nutan ^a   Ozelius, Laurie J ^b   Bragg, D Cristopher ^a  

^a MASSACHUSETTS GENERAL HOSPITAL   (United States)

^b MOUNT SINAI SCHOOL OF MEDICINE   (United States)

Author keywords

dimerization; dystonia; DYT6; leucine zipper; THAP1

Indexed keywords

DNA BINDING PROTEIN; LEUCINE ZIPPER PROTEIN; THAP1 PROTEIN; TRANSCRIPTION FACTOR; UNCLASSIFIED DRUG;

AMINO ACID SEQUENCE; ARTICLE; CARBOXY TERMINAL SEQUENCE; CONTROLLED STUDY; DIMERIZATION; DYSTONIA; EMBRYO; FRAMESHIFT MUTATION; GENE DELETION; GENE MUTATION; GENETIC VARIABILITY; HUMAN; HUMAN CELL; PRIORITY JOURNAL; PROTEIN BINDING; PROTEIN DOMAIN; PROTEIN FAMILY; PROTEIN STRUCTURE; SEQUENCE HOMOLOGY; WILD TYPE;

AMINO ACID SEQUENCE; APOPTOSIS REGULATORY PROTEINS; CELL FRACTIONATION; CELL NUCLEUS; COMPUTER SIMULATION; CYTOSOL; DIMERIZATION; DNA; DNA-BINDING PROTEINS; DYSTONIA MUSCULORUM DEFORMANS; EPITOPES; FLUORESCENT ANTIBODY TECHNIQUE; HUMANS; INDICATORS AND REAGENTS; MODELS, MOLECULAR; MOLECULAR SEQUENCE DATA; MUTATION; NUCLEAR LOCALIZATION SIGNALS; NUCLEAR PROTEINS; PLASMIDS; PROTEIN CONFORMATION; TRANSFECTION; TRANSLOCATION, GENETIC;

EID: 80052387047     PISSN: 00223042     EISSN: 14714159     Source Type: Journal    
DOI: 10.1111/j.1471-4159.2011.07386.x     Document Type: Article

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