X-linked cholestasis in mouse due to mutations of the P4-ATPase ATP11C

Proceedings of the National Academy of Sciences of the United States of America

Volumn 108, Issue 19, 2011, Pages 7890-7895

  Siggs, Owen M ^a   Schnabl, Bernd ^a   Webb, Bill ^b   Beutler, Bruce ^a  

^a SCRIPPS RESEARCH INSTITUTE   (United States)

^b UNIVERSITY OF CALIFORNIA SAN DIEGO   (United States)

Author keywords

Bile acid; Enterohepatic circulation; Gallbladder; Jaundice; Uterus

Indexed keywords

ADENOSINE TRIPHOSPHATASE; ALANINE AMINOTRANSFERASE; ALKALINE PHOSPHATASE; ASPARTATE AMINOTRANSFERASE; ATP11C PROTEIN; ATP8B1 PROTEIN; CHOLIC ACID; LOW DENSITY LIPOPROTEIN; UNCLASSIFIED DRUG;

ANIMAL EXPERIMENT; ANIMAL TISSUE; ARTICLE; B LYMPHOCYTE; BIRTH; BLOOD LEVEL; CELL MATURATION; CHOLESTASIS; CHOLESTEROL BLOOD LEVEL; CONTROLLED STUDY; DIET SUPPLEMENTATION; DYSTOCIA; EXTRACELLULAR MATRIX; GENE MUTATION; HISTOPATHOLOGY; HOMOZYGOSITY; HYPERBILIRUBINEMIA; LIVER FUNCTION TEST; MOUSE; MOUSE MUTANT; NICK END LABELING; NONHUMAN; POLYMERASE CHAIN REACTION; PREVENTION; PRIORITY JOURNAL; QUANTITATIVE ANALYSIS; TOXICITY; X LINKED CHOLESTASIS;

ANIMALS; B-LYMPHOCYTES; BASE SEQUENCE; CHOLESTASIS, INTRAHEPATIC; CHOLIC ACID; DISEASE MODELS, ANIMAL; DNA PRIMERS; DYSTOCIA; FEMALE; GENES, X-LINKED; GENETIC DISEASES, X-LINKED; HOMOZYGOTE; HYPERBILIRUBINEMIA, HEREDITARY; LYMPHOPENIA; MALE; MICE; MICE, INBRED C57BL; MICE, MUTANT STRAINS; MITOCHONDRIAL PROTON-TRANSLOCATING ATPASES; MOLECULAR CHAPERONES; MUTATION; PHENOTYPE; PREGNANCY;

MUS;

EID: 79956363526     PISSN: 00278424     EISSN: 10916490     Source Type: Journal    
DOI: 10.1073/pnas.1104631108     Document Type: Article

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