Cysteamine restores glutathione redox status in cultured cystinotic proximal tubular epithelial cells

Biochimica et Biophysica Acta - Molecular Basis of Disease

Volumn 1812, Issue 6, 2011, Pages 643-651

  Wilmer, Martijn J ^a,b,c   Kluijtmans, Leo A J ^a   van der Velden, Thea J ^a   Willems, Peter H ^c   Scheffer, Peter G ^d   Masereeuw, Rosalinde ^c   Monnens, Leo A ^c   van den Heuvel, Lambertus P ^a,b   Levtchenko, Elena N ^b  

^a RADBOUD UNIVERSITY MEDICAL CENTER   (Netherlands)

^b UNIVERSITY HOSPITALS LEUVEN   (Belgium)

^c RADBOUD UNIVERSITY MEDICAL CENTER   (Netherlands)

^d VU UNIVERSITY MEDICAL CENTER   (Netherlands)

Author keywords

ATP production; Cysteamine; Cystinosis; Glutathione; Oxidative stress; Redox status

Indexed keywords

ADENOSINE TRIPHOSPHATE; ALBUMIN; CYSTINE; DISULFIDE; GLUTATHIONE; MERCAPTAMINE; THIOL;

ARTICLE; CELL PROLIFERATION; CONTROLLED STUDY; CYSTINOSIS; EPITHELIUM CELL; HUMAN; HUMAN CELL; KIDNEY PROXIMAL TUBULE; LIPID PEROXIDATION; MITOCHONDRION; OXIDATION; OXIDATION REDUCTION REACTION; OXIDATIVE STRESS; PHOSPHATE TRANSPORT; PRIORITY JOURNAL; PROTEIN METABOLISM;

ADENOSINE TRIPHOSPHATE; ADOLESCENT; CELL PROLIFERATION; CELLS, CULTURED; CHILD; CHILD, PRESCHOOL; CYSTEAMINE; CYSTINOSIS; EPITHELIAL CELLS; FEMALE; GLUTATHIONE; HUMANS; INFANT; KIDNEY TUBULES, PROXIMAL; MALE; OXIDATION-REDUCTION; REACTIVE OXYGEN SPECIES;

EID: 79954571291     PISSN: 09254439     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.bbadis.2011.02.010     Document Type: Article

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