Impaired activity of the γ-glutamyl cycle in nephropathic cystinosis fibroblasts

Pediatric Research

Volumn 59, Issue 2, 2006, Pages 332-335

  Mannucci, Liliana ^a   Pastore, Anna ^a   Rizzo, Cristiano ^a   Piemonte, Fiorella ^a   Rizzoni, Gianfranco ^a   Emma, Francesco ^a  

^a BAMBINO GESÙ CHILDREN S HOSPITAL   (Italy)

Author keywords

[No Author keywords available]

Indexed keywords

ADENOSINE TRIPHOSPHATE; CYSTEINE; CYSTINE; GLUTAMIC ACID; GLUTATHIONE; HYDROGEN PEROXIDE; PYROGLUTAMIC ACID; CITRATE SYNTHASE; CYTOCHROME C OXIDASE;

APOPTOSIS; ARTICLE; CONTROLLED STUDY; CYSTINOSIS; FIBROBLAST; HUMAN; HUMAN CELL; KIDNEY DISEASE; LYSOSOME; METABOLITE; MITOCHONDRIAL RESPIRATION; NEPHROPATHIC CYSTINOSIS; OXIDATIVE STRESS; PRIORITY JOURNAL; SYNTHESIS; URINARY EXCRETION; ELECTRON TRANSPORT; METABOLISM; PATHOLOGY;

ADENOSINE TRIPHOSPHATE; CITRATE (SI)-SYNTHASE; CYSTINOSIS; ELECTRON TRANSPORT; ELECTRON TRANSPORT COMPLEX IV; FIBROBLASTS; GLUTAMIC ACID; GLUTATHIONE; HUMANS; OXIDATIVE STRESS; PYRROLIDONECARBOXYLIC ACID;

EID: 33646680566     PISSN: 00313998     EISSN: None     Source Type: Journal    
DOI: 10.1203/01.pdr.0000196370.57200.da     Document Type: Article

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