Modulation of CTNS gene expression by intracellular thiols

Free Radical Biology and Medicine

Volumn 48, Issue 7, 2010, Pages 865-872

  Bellomo, Francesco ^a   Corallini, Serena ^a   Pastore, Anna ^a   Palma, Alessia ^a   Laurenzi, Chiara ^a   Emma, Francesco ^a   Taranta, Anna ^a  

^a BAMBINO GESÙ CHILDREN S HOSPITAL   (Italy)

Author keywords

Cystine; Free radicals; Nephropathic cystinosis; Redox state

Indexed keywords

CELL PROTEIN; CYSTEINE; CYSTINE; DISULFIDE; GLUTATHIONE; GLUTATHIONE DISULFIDE; MESSENGER RNA; PROTEIN CTNS; THIOL; UNCLASSIFIED DRUG;

ARTICLE; AUTOSOMAL RECESSIVE DISORDER; CELL DAMAGE; CELL LEVEL; CELLULAR DISTRIBUTION; CONTROLLED STUDY; GENE EXPRESSION REGULATION; GENE OVEREXPRESSION; GENE SILENCING; HUMAN; HUMAN CELL; INTRACELLULAR TRANSPORT; NEPHROPATHIC CYSTINOSIS; OXIDATION REDUCTION STATE; PRIORITY JOURNAL; PROTEIN ANALYSIS; PROTEIN DEPLETION; PROTEIN FUNCTION; PROTEIN SYNTHESIS INHIBITION; REDUCTION KINETICS; REGULATORY MECHANISM;

AMINO ACID TRANSPORT SYSTEMS, NEUTRAL; CELL LINE; CLONING, MOLECULAR; CYSTEINE; CYSTINOSIS; HUMANS; KIDNEY; OXIDATION-REDUCTION; OXIDATIVE STRESS; RNA, SMALL INTERFERING; SULFHYDRYL COMPOUNDS; TRANSGENES;

EID: 77249131170     PISSN: 08915849     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.freeradbiomed.2010.01.011     Document Type: Article

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