-
1
-
-
0026782704
-
Cystine dimethyl ester reduces the forces driving sodium-dependent transport in Llc-Pk1 cells
-
1325121
-
A Ben-Nun N Bashan R Potashnik R Cohen-luria A Moran 1992 Cystine dimethyl ester reduces the forces driving sodium-dependent transport in Llc-Pk1 cells Am J Physiol 263 C516 C520 1325121
-
(1992)
Am J Physiol
, vol.263
-
-
Ben-Nun, A.1
Bashan, N.2
Potashnik, R.3
Cohen-Luria, R.4
Moran, A.5
-
3
-
-
0035206424
-
Severity of oxidative stress generates different mechanisms of endothelial cell death
-
DOI 10.1007/s004410100424
-
A Burlacu V Jinga AV Gafencu M Simionescu 2001 Severity of oxidative stress generates different mechanisms of endothelial cell death Cell Tissue Res 306 409 416 10.1007/s004410100424 11735041 (Pubitemid 33139899)
-
(2001)
Cell and Tissue Research
, vol.306
, Issue.3
, pp. 409-416
-
-
Burlacu, A.1
Jinga, V.2
Gafencu, A.3
Simionescu, M.4
-
5
-
-
0025905226
-
+ -ATPase in the inhibition of proximal tubule transport with intracellular cystine loading
-
10.1172/JCI115103 1847941
-
+ -ATPase in the inhibition of proximal tubule transport with intracellular cystine loading J Clin Invest 87 955 961 10.1172/JCI115103 1847941
-
(1991)
J Clin Invest
, vol.87
, pp. 955-961
-
-
Coor, C.1
Salmon, R.F.2
Quigley, R.3
Marver, D.4
Baum, M.5
-
6
-
-
33646475620
-
Pyruvate is an endogenous anti-inflammatory and anti-oxidant molecule
-
16641887
-
UN Das 2006 Pyruvate is an endogenous anti-inflammatory and anti-oxidant molecule Med Sci Monit 12 RA79 RA84 16641887
-
(2006)
Med Sci Monit
, vol.12
-
-
Das, U.N.1
-
7
-
-
0038037716
-
Phosphotransfer networks and cellular energetics
-
DOI 10.1242/jeb.00426
-
PP Dzeja A Terzic 2003 Phosphotransfer networks and cellular energetics J Exp Biol 206 2039 2047 10.1242/jeb.00426 12756286 (Pubitemid 36761807)
-
(2003)
Journal of Experimental Biology
, vol.206
, Issue.12
, pp. 2039-2047
-
-
Dzeja, P.P.1
Terzic, A.2
-
8
-
-
0033612362
-
Adenylate kinase-catalyzed phosphotransfer in the myocardium: Increased contribution in heart failure
-
10347088
-
PP Dzeja KT Vitkevicius MM Redfield JC Burnettm A Terzic 1999 Adenylate kinase-catalyzed phosphotransfer in the myocardium: increased contribution in heart failure Circ Res 84 1137 1143 10347088
-
(1999)
Circ Res
, vol.84
, pp. 1137-1143
-
-
Dzeja, P.P.1
Vitkevicius, K.T.2
Redfield, M.M.3
Burnettm, J.C.4
Terzic, A.5
-
10
-
-
2442473666
-
Inhibition of pyruvate kinase activity by cystine in brain cortex of rats
-
DOI 10.1016/j.brainres.2004.03.035, PII S0006899304005050
-
LR Feksa A Cornelio CS Dutra-Filho ATS Wyse M Wajner CMD Wannmacher 2004 Inhibition of pyruvate kinase activity by cystine in brain cortex of rats Brain Res 1012 93 100 10.1016/j.brainres.2004.03.035 15158165 (Pubitemid 38648903)
-
(2004)
Brain Research
, vol.1012
, Issue.1-2
, pp. 93-100
-
-
Feksa, L.R.1
Cornelio, A.2
Dutra-Filho, C.S.3
De Souza Wyse, A.T.4
Wajner, M.5
Wannmacher, C.M.D.6
-
11
-
-
14344264450
-
Cysteamine prevents and reverses the inhibition of creatine kinase activity caused by cystine in rat brain cortex
-
DOI 10.1016/j.neuint.2004.11.008
-
RMM Fleck V Rodrigues-Junior J Giacomazzi D Parissoto CS Dutra-Filho ATS Wyse M Wajner CMD Wannmacher 2005 Cysteamine prevents and reverses the inhibition of creatine kinase activity caused by cystine in rat brain cortex Neurochem Int 46 391 397 10.1016/j.neuint.2004.11.008 15737437 (Pubitemid 40292719)
-
(2005)
Neurochemistry International
, vol.46
, Issue.5
, pp. 391-397
-
-
Muller Fleck, R.M.1
Rodrigues, V.2
Giacomazzi, J.3
Parissoto, D.4
Severo Dutra-Filho, C.5
De Souza Wyse, A.T.6
Wajner, M.7
Duval Wannmacher, C.M.8
-
12
-
-
0023494032
-
Effect of cystine dimethyl ester on renal solute handling and isolated renal tubule transport in the rat: A new model Fanconi syndrome
-
10.1016/0026-0495(87)90246-0
-
JW Foreman MA Bowring J Lee B States S Segal 1987 Effect of cystine dimethyl ester on renal solute handling and isolated renal tubule transport in the rat: a new model Fanconi syndrome Metab 36 1185 1191 10.1016/0026-0495(87) 90246-0
-
(1987)
Metab
, vol.36
, pp. 1185-1191
-
-
Foreman, J.W.1
Bowring, M.A.2
Lee, J.3
States, B.4
Segal, S.5
-
14
-
-
0347320495
-
Early oral cysteamine therapy for nephropathic cystinosis
-
10.1007/s00431-003-1349-x
-
WA Gahl 2003 Early oral cysteamine therapy for nephropathic cystinosis Eur J Pediatr 162 1 38 41 10.1007/s00431-003-1349-x
-
(2003)
Eur J Pediatr
, vol.162
, Issue.1
, pp. 38-41
-
-
Gahl, W.A.1
-
15
-
-
0000966393
-
Cystinosis: A disorder of lysosomal membrane transport
-
C.R. Scriver A.L. Beaudet W.S. Sly D. Valle (eds). McGraw-Hill New York
-
Gahl WA, Thoene JG, Schneider JA (2001) Cystinosis: a disorder of lysosomal membrane transport. In: Scriver CR, Beaudet AL, Sly WS, Valle D (eds) The Metabolic & Molecular Bases of Inherited Diseases. McGraw-Hill, New York, pp 5085-5108
-
(2001)
The Metabolic & Molecular Bases of Inherited Diseases
, pp. 5085-5108
-
-
Gahl, W.A.1
Thoene, J.G.2
Schneider, J.A.3
-
17
-
-
0026064054
-
Hydroperoxide initiated chemiluminescence: An assay for oxidative stress in biopsies of heart, liver, and muscle
-
10.1016/0891-5849(91)90002-K
-
FB Gonzalez S Llesuy A Boveris 1991 Hydroperoxide initiated chemiluminescence: an assay for oxidative stress in biopsies of heart, liver, and muscle Free Radic Biol Med 10 93 100 10.1016/0891-5849(91)90002-K
-
(1991)
Free Radic Biol Med
, vol.10
, pp. 93-100
-
-
Gonzalez, F.B.1
Llesuy, S.2
Boveris, A.3
-
20
-
-
70350021177
-
-
Use and interpretation Lawrence Erlbaum Associates Publishers (ed), London
-
Leech NL, Barrett KC, Morgan GA (2005) SPSS for intermediate statistics. Use and interpretation, Lawrence Erlbaum Associates Publishers (ed), London, pp 46-62
-
(2005)
SPSS for Intermediate Statistics
, pp. 46-62
-
-
Leech, N.L.1
Barrett, K.C.2
Morgan, G.A.3
-
21
-
-
33646698007
-
Decreased intracellular ATP content and intact mitochondrial energy generating capacity in human cystinotic fibroblasts
-
DOI 10.1203/01.pdr.0000196334.46940.54, PII 0000645020060200000024
-
EN Levtchenko MJG Wilmer AJM Janssen JB Koenderink EN Levtchenko MJG Wilmer AJM Janssen JB Koenderink AJ Visch PH Willems A Graaf-Hess HJ Blom LP van den Heuvel LA Monnens 2006 Decreased ATP content and intact mitochondrial energy generating capacity in human cystinotic fibroblasts Pediatr Res 59 287 292 10.1203/01.pdr.0000196334.46940.54 16439594 (Pubitemid 43841004)
-
(2006)
Pediatric Research
, vol.59
, Issue.2
, pp. 287-292
-
-
Levtchenko, E.N.1
Wilmer, M.J.G.2
Janssen, A.J.M.3
Koenderink, J.B.4
Visch, H.-J.5
Willems, P.H.G.M.6
De Graaf-Hess, A.7
Blom, H.J.8
Van Den Heuvel, L.P.9
Monnens, L.A.10
-
22
-
-
0021874569
-
Comparison of lipid peroxidation and myocardial damage induced by adriamycin and 40-epiadriamycin in mice
-
3861023
-
SF Llesuy J Milei H Molina 1985 Comparison of lipid peroxidation and myocardial damage induced by adriamycin and 40-epiadriamycin in mice Tumori 71 3 241 249 3861023
-
(1985)
Tumori
, vol.71
, Issue.3
, pp. 241-249
-
-
Llesuy, S.F.1
Milei, J.2
Molina, H.3
-
23
-
-
0022485546
-
Disulphide reduction in lysosomes. the role of cysteine
-
3800880
-
JB Lloyd 1986 Disulphide reduction in lysosomes. The role of cysteine Biochem J 237 1 271 272 3800880
-
(1986)
Biochem J
, vol.237
, Issue.1
, pp. 271-272
-
-
Lloyd, J.B.1
-
24
-
-
71849104860
-
Protein measurement with the Folin phenol reagent
-
14907713
-
OH Lowry NJ Rosebrough AL Farr 1951 Protein measurement with the Folin phenol reagent J Biol Chem 193 265 275 14907713
-
(1951)
J Biol Chem
, vol.193
, pp. 265-275
-
-
Lowry, O.H.1
Rosebrough, N.J.2
Farr, A.L.3
-
26
-
-
0000479830
-
A spectrophotometric method for the determination of creatine phosphokinase and myokinase
-
13260184
-
IT Oliver 1955 A spectrophotometric method for the determination of creatine phosphokinase and myokinase Biochem J 61 1 116 122 13260184
-
(1955)
Biochem J
, vol.61
, Issue.1
, pp. 116-122
-
-
Oliver, I.T.1
-
27
-
-
15344339173
-
Potential role of apoptosis in development of the cystinotic phenotype
-
DOI 10.1007/s00467-004-1712-9
-
MA Park JG Thoene 2005 Potential role of apoptosis in development of the cystinotic phenotype Pediatr Nephrol 20 441 446 10.1007/s00467-004-1712-9 15622500 (Pubitemid 40392614)
-
(2005)
Pediatric Nephrology
, vol.20
, Issue.4
, pp. 441-446
-
-
Park, M.A.1
Thoene, J.G.2
-
28
-
-
0028804534
-
Detection and characterization of a transport system mediating cysteamine entry into human fibroblast lysosomes. Specificity for aminoethylthiol and aminoethylsulfide derivatives
-
10.1074/jbc.270.3.1179 7836377
-
RL Pisoni GY Park VQ Velilla JG Thoene 1995 Detection and characterization of a transport system mediating cysteamine entry into human fibroblast lysosomes. Specificity for aminoethylthiol and aminoethylsulfide derivatives J Biol Chem 270 1179 1184 10.1074/jbc.270.3.1179 7836377
-
(1995)
J Biol Chem
, vol.270
, pp. 1179-1184
-
-
Pisoni, R.L.1
Park, G.Y.2
Velilla, V.Q.3
Thoene, J.G.4
-
29
-
-
0016662185
-
Fluorescent and spin label probes of the environments of the sulfhydryl groups of porcine muscle adenylate kinase
-
163231
-
NC Price M Cohn RH Schirmer 1975 Fluorescent and spin label probes of the environments of the sulfhydryl groups of porcine muscle adenylate kinase J Biol Chem 250 644 652 163231
-
(1975)
J Biol Chem
, vol.250
, pp. 644-652
-
-
Price, N.C.1
Cohn, M.2
Schirmer, R.H.3
-
30
-
-
0034731467
-
Compromised energetics in the adenylate kinase AK1 gene knockout heart under metabolic stress
-
DOI 10.1074/jbc.M007903200
-
D Pucar E Janssen PP Dzeja N Juranic S Macura B Wieringa A Terzic 2000 Compromised energetics in the adenylate kinase AK1 gene knockout heart under metabolic stress J Biol Chem 275 41424 41429 10.1074/jbc.M007903200 11006295 (Pubitemid 32054978)
-
(2000)
Journal of Biological Chemistry
, vol.275
, Issue.52
, pp. 41424-41429
-
-
Pucar, D.1
Janssen, E.2
Dzeja, P.P.3
Juranic, N.4
Macura, S.5
Wieringa, B.6
Terzic, A.7
-
31
-
-
34548391509
-
Promotion of oxidative stress in kidney of rats loaded with cystine dimethyl ester
-
10.1007/s00467-007-0494-2 17534668
-
VC Rech LR Feksa MFA Amaral GW Koch M Wajner CS Dutra-Filho ATS Wyse CMD Wannmacher 2007 Promotion of oxidative stress in kidney of rats loaded with cystine dimethyl ester Pediatr Nephrol 22 1121 1128 10.1007/s00467-007-0494-2 17534668
-
(2007)
Pediatr Nephrol
, vol.22
, pp. 1121-1128
-
-
Rech, V.C.1
Feksa, L.R.2
Amaral, M.F.A.3
Koch, G.W.4
Wajner, M.5
Dutra-Filho, C.S.6
Wyse, A.T.S.7
Wannmacher, C.M.D.8
-
32
-
-
2942642272
-
Cysteamine prevents and reverses the inhibition of pyruvate kinase activity caused by cystine in rat heart
-
15196592
-
TG Rosa ATS Wyse M Wajner CMD Wannmacher 2004 Cysteamine prevents and reverses the inhibition of pyruvate kinase activity caused by cystine in rat heart Biochim Biophys Acta 1689 114 119 15196592
-
(2004)
Biochim Biophys Acta
, vol.1689
, pp. 114-119
-
-
Rosa, T.G.1
Wyse, A.T.S.2
Wajner, M.3
Wannmacher, C.M.D.4
-
33
-
-
0025117493
-
Intracellular cystine loading inhibits transport in the rabbit proximal convoluted tubule
-
10.1172/JCI114443 2298908
-
RF Salmon M Baum 1990 Intracellular cystine loading inhibits transport in the rabbit proximal convoluted tubule J Clin Invest 85 340 344 10.1172/JCI114443 2298908
-
(1990)
J Clin Invest
, vol.85
, pp. 340-344
-
-
Salmon, R.F.1
Baum, M.2
-
34
-
-
0031945551
-
A novel gene encoding an integral membrane protein is mutated in nephropathic cystinosis
-
DOI 10.1038/ng0498-319
-
M Town G Jean S Cherqui M Attard L Forestier S Whitmore D Callen O Gribouval M Broyer G Bates W van't Hoff C Antignac 1998 A novel gene encoding an integral membrane protein is mutated in nephropathic cystinosis Nat Genet 18 319 324 10.1038/ng0498-319 9537412 (Pubitemid 28158158)
-
(1998)
Nature Genetics
, vol.18
, Issue.4
, pp. 319-324
-
-
Town, M.1
Jean, G.2
Cherqui, S.3
Attard, M.4
Forestier, L.5
Whitmore, S.A.6
Gallen, D.F.7
Gribouval, O.8
Broyer, M.9
Bates, G.P.10
Hoff, W.V.11
Antignac, C.12
-
35
-
-
0014267162
-
Amino acid sequences around the thiol groups of myokinase
-
5641885
-
AG Weeds L Noda 1968 Amino acid sequences around the thiol groups of myokinase Biochem J 107 311 312 5641885
-
(1968)
Biochem J
, vol.107
, pp. 311-312
-
-
Weeds, A.G.1
Noda, L.2
-
36
-
-
28444493318
-
Nucleoside triphosphate synthesis catalysed by adenylate kinase is ADP dependent
-
DOI 10.1016/j.abb.2005.10.003, PII S000398610500411X
-
M Willemoes M Kilstrup 2005 Nucleoside triphosphate synthesis catalysed by adenylate kinase is ADP dependent Arch Biochem Biophys 444 195 199 10.1016/j.abb.2005.10.003 16297370 (Pubitemid 41728351)
-
(2005)
Archives of Biochemistry and Biophysics
, vol.444
, Issue.2
, pp. 195-199
-
-
Willemoes, M.1
Kilstrup, M.2
-
37
-
-
26444571755
-
Elevated oxidized glutathione in cystinotic proximal tubular epithelial cells
-
DOI 10.1016/j.bbrc.2005.09.094, PII S0006291X05020735
-
MJ Wilmer A de Graaf-Hess HJ Blom HB Dijkman LA Monnens LP van den Heuvel EM Levtchenko 2005 Elevated oxidized glutathione in cystinotic proximal tubular epithelial cells Biochem Biophys Res Commun 337 610 614 10.1016/j.bbrc.2005.09. 094 16202976 (Pubitemid 41429328)
-
(2005)
Biochemical and Biophysical Research Communications
, vol.337
, Issue.2
, pp. 610-614
-
-
Wilmer, M.J.G.1
De Graaf-Hess, A.2
Blom, H.J.3
Dijkman, H.B.P.M.4
Monnens, L.A.5
Van Den Heuvel, L.P.6
Levtchenko, E.N.7
-
38
-
-
34547639333
-
Cystine dimethylester model of cystinosis: Still reliable?
-
DOI 10.1203/PDR.0b013e31809fd9a7, PII 0000645020070800000008
-
MJ Wilmer PH Willems S Verkaart HJ Visch A de Graaf-Hess HJ Blom LA Monnens LP van den Heuvel EN Levtchenko 2007 Cystine dimethylester model of cystinosis: still reliable? Pediatr Res 62 151 155 10.1203/PDR.0b013e31809fd9a7 17597653 (Pubitemid 47205712)
-
(2007)
Pediatric Research
, vol.62
, Issue.2
, pp. 151-155
-
-
Wilmer, M.J.1
Willems, P.H.2
Verkaart, S.3
Visch, H.-J.4
De Graaf-Hess, A.5
Blom, H.J.6
Monnens, L.A.7
Van Den Heuvel, L.P.8
Levtchenko, E.N.9
|