Glutathione precursors replenish decreased glutathione pool in cystinotic cell lines

Biochemical and Biophysical Research Communications

Volumn 324, Issue 1, 2004, Pages 231-235

  Chol, Marie ^a   Nevo, Nathalie ^a   Cherqui, Stéphanie ^a   Antignac, Corinne ^a   Rustin, Pierre ^a  

^a INSERM   (France)

Author keywords

Cystinosis; Glutathione; Human skin fibroblasts; Mitochondria; Superoxide dismutase

Indexed keywords

CYSTINE; GLUTATHIONE; SUPEROXIDE DISMUTASE;

ARTICLE; CELL GROWTH; CELL LINE; CELL PROTECTION; CELLULAR DISTRIBUTION; CONTROLLED STUDY; CYSTINOSIS; CYTOSOL; ENZYME INDUCTION; GENE MUTATION; HUMAN; HUMAN CELL; LYSOSOME STORAGE DISEASE; MUTAGENESIS; OXIDATIVE STRESS; PATHOGENESIS; PRECURSOR; PRIORITY JOURNAL; PROTEIN LOCALIZATION;

ADOLESCENT; ANIMALS; CELL LINE; CHILD; CYSTINE; CYSTINOSIS; FIBROBLASTS; GLUTATHIONE; GLYCOPROTEINS; HUMANS; INFANT; MEMBRANE PROTEINS; MEMBRANE TRANSPORT PROTEINS; MUTATION; OXIDATION-REDUCTION; PROTEIN PRECURSORS; SUPEROXIDE DISMUTASE;

EID: 4744368742     PISSN: 0006291X     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.bbrc.2004.09.033     Document Type: Article

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