PLP/DM20 Expression and turnover in a transgenic mouse model of pelizaeus-merzbacher disease

GLIA

Volumn 58, Issue 14, 2010, Pages 1727-1738

  Karim, Saadia A ^a   Barrie, Jennifer A ^b   Mcculloch, Mailis C ^b   Montague, Paul ^b   Edgar, Julia M ^b   Iden, Debrah L ^b   Anderson, Thomas J ^b   Nave, Klaus Armin ^c   Griffiths, Ian R ^b   McLaughlin, Mark ^b  

^a BEATSON INSTITUTE FOR CANCER RESEARCH   (United Kingdom)

^b UNIVERSITY OF GLASGOW   (United Kingdom)

^c MAX PLANCK INSTITUTE OF EXPERIMENTAL MEDICINE   (Germany)

Author keywords

Autophagy; Myelin; Myelin basic protein; Oligodendrocyte; Proteasome

Indexed keywords

MEMBRANE PROTEIN; PROTEASOME INHIBITOR; PROTEOLIPID PROTEIN 1; RAPAMYCIN; SMALL INTERFERING RNA; UNCLASSIFIED DRUG;

ANIMAL CELL; ANIMAL CELL CULTURE; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; AUTOPHAGY; BRAIN SLICE; ENDOCYTOSIS; GENE DOSAGE; GENE DUPLICATION; IN VITRO STUDY; LIPID RAFT; MALE; MOUSE; MYELIN SHEATH; NONHUMAN; OLIGODENDROGLIA; PELIZAEUS MERZBACHER DISEASE; PRIORITY JOURNAL; PROTEIN ANALYSIS; PROTEIN DEGRADATION; PROTEIN EXPRESSION; PROTEIN METABOLISM; PROTEIN PROCESSING; TRANSGENIC MOUSE;

ANIMALS; CELLS, CULTURED; DISEASE MODELS, ANIMAL; DOWN-REGULATION; GENETIC PREDISPOSITION TO DISEASE; HUMANS; MALE; MICE; MICE, INBRED C57BL; MICE, TRANSGENIC; MYELIN PROTEOLIPID PROTEIN; MYELIN SHEATH; ORGAN CULTURE TECHNIQUES; PELIZAEUS-MERZBACHER DISEASE; RNA INTERFERENCE; VACUOLES;

EID: 78349232686     PISSN: 08941491     EISSN: 10981136     Source Type: Journal    
DOI: 10.1002/glia.21043     Document Type: Article

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