Genetic background influences UPR but not PLP processing in the rumpshaker model of PMD/SPG2

Neurochemical Research

Volumn 32, Issue 2, 2007, Pages 167-176

  McLaughlin, M ^a   Karim, S A ^a   Montague, P ^a   Barrie, J A ^a   Kirkham, D ^a   Griffiths, I R ^a   Edgar, J M ^a  

^a UNIVERSITY OF GLASGOW   (United Kingdom)

Author keywords

CHOP; Misfolded protein; Myelin; Oligodendrocyte; Pelizaeus Merzbacher disease; Proteolipid protein; Rumpshaker

Indexed keywords

DM20 PROTEIN; GLUCOSE REGULATED PROTEIN 78; GROWTH ARREST AND DNA DAMAGE INDUCIBLE PROTEIN 153; ISOPROTEIN; MYELIN; PROTEASOME; PROTEIN; PROTEOLIPID PROTEIN; UNCLASSIFIED DRUG; X BOX BINDING PROTEIN 1;

ANIMAL CELL; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; C3H MOUSE; C57BL 6 MOUSE; FEMALE; GENE MUTATION; GENETICS; MALE; MOUSE; MOUSE MUTANT; MOUSE STRAIN; NONHUMAN; NUCLEOTIDE SEQUENCE; PELIZAEUS MERZBACHER DISEASE; PHENOTYPE; PHENOTYPIC VARIATION; PRIORITY JOURNAL; PROTEIN DEGRADATION; PROTEIN PROCESSING; PROTEIN SYNTHESIS; RUMPSHAKER; SPASTIC PARAPLEGIA; SPASTIC PARAPLEGIA TYPE 2; WILD TYPE;

ACTIVATING TRANSCRIPTION FACTOR 3; ANIMALS; DISEASE MODELS, ANIMAL; DNA-BINDING PROTEINS; HEAT-SHOCK PROTEINS; MICE; MICE, INBRED C3H; MICE, INBRED C57BL; MICE, NEUROLOGIC MUTANTS; MOLECULAR CHAPERONES; MYELIN PROTEOLIPID PROTEIN; MYELIN SHEATH; NERVE TISSUE PROTEINS; NUCLEAR PROTEINS; PELIZAEUS-MERZBACHER DISEASE; PROTEIN FOLDING; TRANSCRIPTION FACTOR CHOP;

MUS;

EID: 33846906017     PISSN: 03643190     EISSN: None     Source Type: Journal    
DOI: 10.1007/s11064-006-9122-y     Document Type: Article

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