Agent strain variation in human prion disease: Insights from a molecular and pathological review of the National Institutes of Health series of experimentally transmitted disease

Brain

Volumn 133, Issue 10, 2010, Pages 3030-3042

  Parchi, Piero ^a   Cescatti, Maura ^a   Notari, Silvio ^a   Schulz Schaeffer, Walter J ^b   Capellari, Sabina ^a   Giese, Armin ^c   Zou, Wen Quan ^d   Kretzschmar, Hans ^c   Ghetti, Bernardino ^e   Brown, Paul ^f  

^a UNIVERSITY OF BOLOGNA   (Italy)

^b UNIVERSITY MEDICAL CENTER GÖTTINGEN   (Germany)

^c UNIVERSITY OF MUNICH   (Germany)

^d CASE WESTERN RESERVE UNIVERSITY   (United States)

^e INDIANA UNIVERSITY SCHOOL OF MEDICINE   (United States)

^f CEA DSV iMETI SEPIA   (France)

Author keywords

neurodegenerative disorders; neuropathology; phenotype; prion diseases; strain typing

Indexed keywords

PRION PROTEIN;

ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; CERCOPITHECIDAE; CREUTZFELDT JAKOB DISEASE; DISEASE TRANSMISSION; EXPERIMENTAL MONKEY; GENETIC ANALYSIS; HUMAN; HUMAN TISSUE; KURU; NEUROPATHOLOGY; NONHUMAN; PHENOTYPE; PRIORITY JOURNAL; PROTEIN VARIANT; SPIDER MONKEY; SQUIRREL MONKEY; ANIMAL; ATELIDAE; BRAIN; CEBUS; CHLOROCEBUS AETHIOPS; GENETICS; PATHOLOGY; TRANSMISSION; WESTERN BLOTTING;

ANIMALS; ATELINAE; BLOTTING, WESTERN; BRAIN; CEBUS; CERCOPITHECUS AETHIOPS; CREUTZFELDT-JAKOB SYNDROME; HUMANS; KURU; PRPSC PROTEINS; SAIMIRI;

EID: 77957660770     PISSN: 00068950     EISSN: 14602156     Source Type: Journal    
DOI: 10.1093/brain/awq234     Document Type: Article

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