-
2
-
-
0027319326
-
Mice devoid of PrP are resistant to scrapie
-
Büeler H, Aguzzi A, Sailer A, et al. Mice devoid of PrP are resistant to scrapie. Cell 1993;73:1339-1347.
-
(1993)
Cell
, vol.73
, pp. 1339-1347
-
-
Büeler, H.1
Aguzzi, A.2
Sailer, A.3
-
3
-
-
0025944507
-
Secondary structure analysis of the scrapie-associated protein PrP27-30 in water by infrared spectroscopy
-
Caughey BW, Dong A, Bhat KS, et al. Secondary structure analysis of the scrapie-associated protein PrP27-30 in water by infrared spectroscopy. Biochemistry 1991;30:7672-7680.
-
(1991)
Biochemistry
, vol.30
, pp. 7672-7680
-
-
Caughey, B.W.1
Dong, A.2
Bhat, K.S.3
-
4
-
-
0027332116
-
Conversion of alpha-helices into beta-sheets features in the formation of the scrapie prion proteins
-
Pan KM, Baldwin M, Nguyen J, et al. Conversion of alpha-helices into beta-sheets features in the formation of the scrapie prion proteins. Proc Natl Acad Sci USA 1993;90:10962-10966.
-
(1993)
Proc Natl Acad Sci USA
, vol.90
, pp. 10962-10966
-
-
Pan, K.M.1
Baldwin, M.2
Nguyen, J.3
-
5
-
-
28444457804
-
Quantitative traits of prion strains are enciphered in the conformation of the prion protein
-
Safar J, Cohen FE, Prusiner SB. Quantitative traits of prion strains are enciphered in the conformation of the prion protein. Arch Virol Suppl 2000;16:227-235.
-
(2000)
Arch Virol Suppl
, vol.16
, pp. 227-235
-
-
Safar, J.1
Cohen, F.E.2
Prusiner, S.B.3
-
6
-
-
0020490156
-
Identification of a protein that purifies with the scrapie prion
-
Bolton DC, McKinley MP, Prusiner SB. Identification of a protein that purifies with the scrapie prion. Science 1982;218:1309-1311.
-
(1982)
Science
, vol.218
, pp. 1309-1311
-
-
Bolton, D.C.1
McKinley, M.P.2
Prusiner, S.B.3
-
7
-
-
0141514771
-
Sporadic and familial CJD: Classification and characterisation
-
Gambetti P, Kong Q, Zou W, et al. Sporadic and familial CJD: classification and characterisation. Br Med Bull 2003;66:213-239.
-
(2003)
Br Med Bull
, vol.66
, pp. 213-239
-
-
Gambetti, P.1
Kong, Q.2
Zou, W.3
-
8
-
-
84881724182
-
Pathology and genetics of human prion diseases
-
Hoernlimann B, Riesner D, Kretzschmar H eds, De Gruyter: Berlin/New York
-
Kretzschmar HA, Parchi P. Pathology and genetics of human prion diseases. In: Hoernlimann B, Riesner D, Kretzschmar H (eds). Prions in Humans and Animals. De Gruyter: Berlin/New York, 2007, pp 287-305.
-
(2007)
Prions in Humans and Animals
, pp. 287-305
-
-
Kretzschmar, H.A.1
Parchi, P.2
-
9
-
-
0026099887
-
The disease characteristics of different strains of scrapie in Sinc congenic mouse lines: Implications for the nature of the agent and host control of pathogenesis
-
Bruce ME, McConnell I, Fraser H, et al. The disease characteristics of different strains of scrapie in Sinc congenic mouse lines: implications for the nature of the agent and host control of pathogenesis. J Gen Virol 1991;72:595-603.
-
(1991)
J Gen Virol
, vol.72
, pp. 595-603
-
-
Bruce, M.E.1
McConnell, I.2
Fraser, H.3
-
10
-
-
0025820942
-
Homozygous prion protein genotype predisposes to sporadic Creutzfeldt-Jakob disease
-
Palmer MS, Dryden AJ, Hughes JT, et al. Homozygous prion protein genotype predisposes to sporadic Creutzfeldt-Jakob disease. Nature 1991;352:340-342.
-
(1991)
Nature
, vol.352
, pp. 340-342
-
-
Palmer, M.S.1
Dryden, A.J.2
Hughes, J.T.3
-
11
-
-
1842644947
-
Inherited prion diseases
-
Prusiner SB ed, 2nd edn. Cold Spring Harbor: New York
-
Kong Q, Surewicz WK, Petersen RB, et al. Inherited prion diseases. In: Prusiner SB (ed). Prion Biology and Diseases, 2nd edn. Cold Spring Harbor: New York, 2004, pp 673-775.
-
(2004)
Prion Biology and Diseases
, pp. 673-775
-
-
Kong, Q.1
Surewicz, W.K.2
Petersen, R.B.3
-
12
-
-
0035903461
-
Changing a single amino acid in the N-terminus of murine PrP alters TSE incubation time across three species barriers
-
Barron RM, Thomson V, Jamieson E, et al. Changing a single amino acid in the N-terminus of murine PrP alters TSE incubation time across three species barriers. EMBO J 2001;20:5070-5078.
-
(2001)
EMBO J
, vol.20
, pp. 5070-5078
-
-
Barron, R.M.1
Thomson, V.2
Jamieson, E.3
-
13
-
-
12644272790
-
Evidence for the conformation of the pathologic isoform of the prion protein enciphering and propagating prion diversity
-
Telling GC, Parchi P, DeArmond SJ, et al. Evidence for the conformation of the pathologic isoform of the prion protein enciphering and propagating prion diversity. Science 1996;274:2079-2082.
-
(1996)
Science
, vol.274
, pp. 2079-2082
-
-
Telling, G.C.1
Parchi, P.2
DeArmond, S.J.3
-
14
-
-
0030775632
-
Transmissions to mice indicate that 'new variant' CJD is caused by the BSE agent
-
Bruce ME, Will RG, Ironside JW, et al. Transmissions to mice indicate that 'new variant' CJD is caused by the BSE agent. Nature 1997;389:498-501.
-
(1997)
Nature
, vol.389
, pp. 498-501
-
-
Bruce, M.E.1
Will, R.G.2
Ironside, J.W.3
-
15
-
-
1942446629
-
Agent strain variation in human prion diseases: Insights from transmission to primates
-
Iqbal K, Swaab DF, Winblad D, Wisniewski HM eds, Wiley J & Sons Ltd: Chichester, UK
-
Parchi P, Brown P, Capellari P, et al. Agent strain variation in human prion diseases: insights from transmission to primates. In: Iqbal K, Swaab DF, Winblad D, Wisniewski HM (eds). Alzheimer' s Disease and Related Disorders: Etiology, Pathogenesis, and Therapeutics. Wiley J & Sons Ltd: Chichester, UK, 1999, pp 561-567.
-
(1999)
Alzheimer' s Disease and Related Disorders: Etiology, Pathogenesis, and Therapeutics
, pp. 561-567
-
-
Parchi, P.1
Brown, P.2
Capellari, P.3
-
16
-
-
0037447071
-
Abbreviated incubation times for human prions in mice expressing a chimeric mouse - human prion protein transgene
-
Korth C, Kaneko K, Groth D, et al. Abbreviated incubation times for human prions in mice expressing a chimeric mouse - human prion protein transgene. Proc Natl Acad Sci USA 2003;100:4784-4789.
-
(2003)
Proc Natl Acad Sci USA
, vol.100
, pp. 4784-4789
-
-
Korth, C.1
Kaneko, K.2
Groth, D.3
-
17
-
-
0022447893
-
Immunological comparison of scrapie-associated fibrils isolated from animals infected with four different scrapie strains
-
Kascsak RJ, Rubenstein R, Merz PA, et al. Immunological comparison of scrapie-associated fibrils isolated from animals infected with four different scrapie strains. J Virol 1986;59:676-683.
-
(1986)
J Virol
, vol.59
, pp. 676-683
-
-
Kascsak, R.J.1
Rubenstein, R.2
Merz, P.A.3
-
18
-
-
0028043661
-
Distinct PrP properties suggest the molecular basis of strain variation in transmissible mink encephalopathy
-
Bessen RA, Marsh RF. Distinct PrP properties suggest the molecular basis of strain variation in transmissible mink encephalopathy. J Virol 1994;68:7859-7868.
-
(1994)
J Virol
, vol.68
, pp. 7859-7868
-
-
Bessen, R.A.1
Marsh, R.F.2
-
19
-
-
0028351904
-
Fatal familial insomnia and familial Creutzfeldt-Jakob disease: Different prion proteins determined by a DNA polymorphism
-
Monari L, Chen SG, Brown P, et al. Fatal familial insomnia and familial Creutzfeldt-Jakob disease: different prion proteins determined by a DNA polymorphism. Proc Natl Acad Sci USA 1994;91:2839-2842.
-
(1994)
Proc Natl Acad Sci USA
, vol.91
, pp. 2839-2842
-
-
Monari, L.1
Chen, S.G.2
Brown, P.3
-
20
-
-
8944259890
-
Molecular basis of phenotypic variability in sporadic Creutzfeldt-Jakob disease
-
Parchi P, Castellani R, Capellari S, et al. Molecular basis of phenotypic variability in sporadic Creutzfeldt-Jakob disease. Ann Neurol 1996;39:767-778.
-
(1996)
Ann Neurol
, vol.39
, pp. 767-778
-
-
Parchi, P.1
Castellani, R.2
Capellari, S.3
-
22
-
-
0029831213
-
Molecular analysis of prion strain variation and the aetiology of 'new variant' CJD
-
Collinge J, Sidle KCL, Meads J, et al. Molecular analysis of prion strain variation and the aetiology of 'new variant' CJD. Nature 1996;383:685-690.
-
(1996)
Nature
, vol.383
, pp. 685-690
-
-
Collinge, J.1
Sidle, K.C.L.2
Meads, J.3
-
24
-
-
0031720905
-
Sc molecules with different conformations
-
Sc molecules with different conformations. Nat Med 1998;4:1157-1165.
-
(1998)
Nat Med
, vol.4
, pp. 1157-1165
-
-
Safar, J.1
Wille, H.2
Itri, V.3
-
25
-
-
0033610870
-
Strain-dependent differences in beta-sheet conformations of abnormal prion protein
-
Caughey B, Raymond GJ, Bessen RA. Strain-dependent differences in beta-sheet conformations of abnormal prion protein. J Biol Chem 1998;273:32230-32235.
-
(1998)
J Biol Chem
, vol.273
, pp. 32230-32235
-
-
Caughey, B.1
Raymond, G.J.2
Bessen, R.A.3
-
26
-
-
35349004422
-
History and state of the art of PrP-res 'typing' in Creutzfeldt-Jakob disease
-
Kitamoto T ed, Springer-Verlag: Tokyo
-
Parchi P, Notari S, Stramiello R, et al. History and state of the art of PrP-res 'typing' in Creutzfeldt-Jakob disease. In: Kitamoto T (ed). Prions: Food and Drug Safety. Springer-Verlag: Tokyo, 2005, pp 77-96.
-
(2005)
Prions: Food and Drug Safety
, pp. 77-96
-
-
Parchi, P.1
Notari, S.2
Stramiello, R.3
-
27
-
-
34447123223
-
Atypical transmissible spongiform encephalopathies (TSEs) in ruminants
-
Baron T, Biacabe AG, Arsac JN, et al. Atypical transmissible spongiform encephalopathies (TSEs) in ruminants. Vaccine 2007;25:5625-5630.
-
(2007)
Vaccine
, vol.25
, pp. 5625-5630
-
-
Baron, T.1
Biacabe, A.G.2
Arsac, J.N.3
-
28
-
-
12944253111
-
Genetic influence on the structural variations of the abnormal prion protein
-
Parchi P, Zou W, Wang W, et al. Genetic influence on the structural variations of the abnormal prion protein. Proc Natl Acad Sci USA 2000;97:10168-10172.
-
(2000)
Proc Natl Acad Sci USA
, vol.97
, pp. 10168-10172
-
-
Parchi, P.1
Zou, W.2
Wang, W.3
-
29
-
-
0032816292
-
Classification of sporadic Creutzfeldt-Jakob disease based on molecular and phenotypic analysis of 300 subjects
-
Parchi P, Giese A, Capellari S, et al. Classification of sporadic Creutzfeldt-Jakob disease based on molecular and phenotypic analysis of 300 subjects. Ann Neurol 1999;46:224-233.
-
(1999)
Ann Neurol
, vol.46
, pp. 224-233
-
-
Parchi, P.1
Giese, A.2
Capellari, S.3
-
32
-
-
2542618458
-
Prion protein heterogeneity in sporadic but not variant Creutzfeldt-Jakob disease: UK cases 1991-2002
-
Head MW, Bunn TJ, Bishop MT, et al. Prion protein heterogeneity in sporadic but not variant Creutzfeldt-Jakob disease: UK cases 1991-2002. Ann Neurol 2004;55:851-859.
-
(2004)
Ann Neurol
, vol.55
, pp. 851-859
-
-
Head, M.W.1
Bunn, T.J.2
Bishop, M.T.3
-
35
-
-
30344438495
-
Detection of type 1 prion protein in variant Creutzfeldt-Jakob disease
-
Yull HM, Ritchie DL, Langeveld JP, et al. Detection of type 1 prion protein in variant Creutzfeldt-Jakob disease. Am J Pathol 2006;168:151-157.
-
(2006)
Am J Pathol
, vol.168
, pp. 151-157
-
-
Yull, H.M.1
Ritchie, D.L.2
Langeveld, J.P.3
-
36
-
-
0032976574
-
A sporadic prion disease mimicking fatal familial insomnia
-
Parchi P, Capellari S, Chin S, et al. A sporadic prion disease mimicking fatal familial insomnia. Neurology 1999;52:1757-1763.
-
(1999)
Neurology
, vol.52
, pp. 1757-1763
-
-
Parchi, P.1
Capellari, S.2
Chin, S.3
-
37
-
-
0023499868
-
Mouse polyclonal and monoclonal antibody to scrapie-associated fibril proteins
-
Kascsak RJ, Rubenstein R, Merz PA, et al. Mouse polyclonal and monoclonal antibody to scrapie-associated fibril proteins. J Virol 1987;61:3688-3693.
-
(1987)
J Virol
, vol.61
, pp. 3688-3693
-
-
Kascsak, R.J.1
Rubenstein, R.2
Merz, P.A.3
-
38
-
-
33747386522
-
Rapid and discriminatory diagnosis of scrapie and BSE in retro-pharyngeal lymph nodes of sheep
-
Langeveld JPM, Jacobs JG, Erkens JH, et al. Rapid and discriminatory diagnosis of scrapie and BSE in retro-pharyngeal lymph nodes of sheep. BMC Vet Res 2006;2:19.
-
(2006)
BMC Vet Res
, vol.2
, pp. 19
-
-
Langeveld, J.P.M.1
Jacobs, J.G.2
Erkens, J.H.3
-
40
-
-
0036938752
-
Differentiation of prion protein glycoforms from naturally occurring sheep scrapie, sheep-passaged scrapie strains (CH1641 and SSBP1), bovine spongiform encephalopathy (9BSE) cases and Romney and Cheviot breed sheep experimentally inoculated with BSE using two monoclonal antibodies
-
Stack MJ, Chaplin MJ, Clark J. Differentiation of prion protein glycoforms from naturally occurring sheep scrapie, sheep-passaged scrapie strains (CH1641 and SSBP1), bovine spongiform encephalopathy (9BSE) cases and Romney and Cheviot breed sheep experimentally inoculated with BSE using two monoclonal antibodies. Acta Neuropathol (Berl.) 2002;104:279-286.
-
(2002)
Acta Neuropathol (Berl.)
, vol.104
, pp. 279-286
-
-
Stack, M.J.1
Chaplin, M.J.2
Clark, J.3
-
41
-
-
12144291345
-
Discrimination between scrapie and bovine spongiform encephalopathy in sheep by molecular size, immunoreactivity, and glycoprofile of prion protein
-
Thuring CMA, Erkens JHF, Jacobs JG, et al. Discrimination between scrapie and bovine spongiform encephalopathy in sheep by molecular size, immunoreactivity, and glycoprofile of prion protein. J Clin Microbiol 2004;42:972-980.
-
(2004)
J Clin Microbiol
, vol.42
, pp. 972-980
-
-
Thuring, C.M.A.1
Erkens, J.H.F.2
Jacobs, J.G.3
-
43
-
-
33846103823
-
Sheep-passaged BSE agent exhibits altered patho-biological properties in bovine-PrP transgenic mice
-
Espinosa JC, Andréoletti O, Castilla J, et al. Sheep-passaged BSE agent exhibits altered patho-biological properties in bovine-PrP transgenic mice. J Virol 2007;81:835-843.
-
(2007)
J Virol
, vol.81
, pp. 835-843
-
-
Espinosa, J.C.1
Andréoletti, O.2
Castilla, J.3
-
44
-
-
0029042656
-
Regional distribution of protease-resistant prion protein in fatal familial insomnia
-
Parchi P, Castellani R, Cortelli P, et al. Regional distribution of protease-resistant prion protein in fatal familial insomnia. Ann Neurol 1995;38:21-29.
-
(1995)
Ann Neurol
, vol.38
, pp. 21-29
-
-
Parchi, P.1
Castellani, R.2
Cortelli, P.3
|