Incidence and spectrum of sporadic Creutzfeldt-Jakob disease variants with mixed phenotype and co-occurrence of PrPSc types: An updated classification

Acta Neuropathologica

Volumn 118, Issue 5, 2009, Pages 659-671

  Parchi, Piero ^a   Strammiello, Rosaria ^a   Notari, Silvio ^a   Giese, Armin ^b   Langeveld, Jan P M ^c   Ladogana, Anna ^d   Zerr, Inga ^e   Roncaroli, Federico ^f   Cras, Patrich ^g   Ghetti, Bernardino ^h   Pocchiari, Maurizio ^d   Kretzschmar, Hans ^b   Capellari, Sabina ^a  

^a UNIVERSITY OF BOLOGNA   (Italy)

^b UNIVERSITY OF MUNICH   (Germany)

^c WAGENINGEN UNIVERSITY   (Netherlands)

^d ISTITUTO SUPERIORE DI SANITÀ   (Italy)

^e UNIVERSITY OF GÖTTINGEN   (Germany)

^f IMPERIAL COLLEGE LONDON   (United Kingdom)

^g UNIVERSITY OF ANTWERP   (Belgium)

^h INDIANA UNIVERSITY   (United States)

Author keywords

Brain mapping; Classification; Molecular typing; Neurodegeneration; Prion protein

Indexed keywords

GENOMIC DNA; PRION PROTEIN;

ADULT; AGED; ARTICLE; BRAIN TISSUE; CLINICAL FEATURE; CONTROLLED STUDY; CREUTZFELDT JAKOB DISEASE; DISEASE CLASSIFICATION; GENETIC POLYMORPHISM; HUMAN; HUMAN TISSUE; IMMUNOHISTOCHEMISTRY; KURU; MAJOR CLINICAL STUDY; MOLECULAR TYPING; NEUROPATHOLOGY; PHENOTYPIC VARIATION; PRIORITY JOURNAL; PROTEIN AGGREGATION;

AGED; AGED, 80 AND OVER; BRAIN; CREUTZFELDT-JAKOB SYNDROME; DNA MUTATIONAL ANALYSIS; FEMALE; HUMANS; INCIDENCE; MALE; METHIONINE; MIDDLE AGED; NEUROLOGIC EXAMINATION; PHENOTYPE; PRPSC PROTEINS; RETROSPECTIVE STUDIES; SENILE PLAQUES; VALINE;

EID: 70449524296     PISSN: 00016322     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00401-009-0585-1     Document Type: Article

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