Induction of S100B secretion in C6 astroglial cells by the major metabolites accumulating in glutaric acidemia type I

Metabolic Brain Disease

Volumn 25, Issue 2, 2010, Pages 191-198

  Quincozes Santos, André ^a   Rosa, Rafael Borba ^a   Leipnitz, Guilhian ^a   De Souza, Daniela Fraga ^a   Seminotti, Bianca ^a   Wajner, Moacir ^a,b   Gonçalves, Carlos Alberto ^a  

^a FEDERAL UNIVERSITY OF RIO GRANDE DO SUL   (Brazil)

^b HOSPITAL DE CLÍNICAS DE PORTO ALEGRE   (Brazil)

Author keywords

3 hydroxyglutaric acid; Astroglial cells; Glutaric acid; Glutaric acidemia type I; Oxidative stress; S100B protein

Indexed keywords

3 HYDROXYGLUTARIC ACID; CARBOXYLIC ACID; GLUTARIC ACID; GLUTATHIONE; PROTEIN S100B; THIOBARBITURIC ACID REACTIVE SUBSTANCE; UNCLASSIFIED DRUG;

ANIMAL CELL; ARTICLE; ASTROCYTE; CELL ACTIVATION; CELL ACTIVITY; CELL FREE SYSTEM; CELL LINEAGE; CELL VIABILITY; CONTROLLED STUDY; ENZYME DEFICIENCY; GLIOMA CELL; GLUTARIC ACIDEMIA TYPE I; LIPID PEROXIDATION; METABOLITE; NONHUMAN; OXIDATIVE STRESS; PROTEIN DETERMINATION; PROTEIN SECRETION; RAT;

AMINO ACID METABOLISM, INBORN ERRORS; ANIMALS; ASTROCYTES; ATROPHY; BRAIN DISEASES, METABOLIC; CELL LINE, TUMOR; CORPUS STRIATUM; GLIOSIS; GLUTARATES; GLUTARYL-COA DEHYDROGENASE; GLUTATHIONE; LIPID PEROXIDATION; NERVE GROWTH FACTORS; OXIDATIVE STRESS; RATS; S100 PROTEINS; THIOBARBITURIC ACID REACTIVE SUBSTANCES;

RATTUS;

EID: 77954089210     PISSN: 08857490     EISSN: None     Source Type: Journal    
DOI: 10.1007/s11011-010-9203-0     Document Type: Article

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