Different proteolipid protein mutants exhibit unique metabolic defects

ASN Neuro

Volumn 1, Issue 3, 2009, Pages 165-180

  Hüttemann, Maik ^a   Zhang, Zhan ^a   Mullins, Chadwick ^a   Bessert, Denise ^a   Lee, Icksoo ^a   Nave, Klaus Armin ^b   Appikatla, Sunita ^a   Skoff, Robert P ^a  

^a WAYNE STATE UNIVERSITY SCHOOL OF MEDICINE   (United States)

^b MAX PLANCK INSTITUTE OF EXPERIMENTAL MEDICINE   (Germany)

Author keywords

Mitochondrion; Oligodendrocyte; Oxidative phosphorylation; Pelizaeus Merzbacher disease, Plp1 mutant

Indexed keywords

ADENOSINE TRIPHOSPHATE; CYTOCHROME C OXIDASE; PROTEOLIPID PROTEIN; PROTEOLIPID PROTEIN 1; UNCLASSIFIED DRUG;

AMINO TERMINAL SEQUENCE; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; DISORDERS OF MITOCHONDRIAL FUNCTIONS; FEMALE; GENE DUPLICATION; GENE INSERTION; HISTOCHEMISTRY; MALE; METABOLIC DISORDER; MISSENSE MUTATION; MITOCHONDRIAL MEMBRANE POTENTIAL; MOUSE; NONHUMAN; PROTEIN LOCALIZATION; PROTEIN MOTIF;

EID: 77953397090     PISSN: None     EISSN: 17590914     Source Type: Journal    
DOI: 10.1042/AN20090028     Document Type: Article

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